Juvenile onset psoriatic arthritis in a patient with X-linked agammaglobulinemia (Bruton's disease)

被引:4
|
作者
Palazzi, C
D'Amico, E
Cacciatore, P
Pennese, E
Petricca, A
Olivieri, I
机构
[1] Villa Pini Clin, Div Rheumatol, Chieti, Italy
[2] Spirito Santo Hosp, Div Internal Med 1, Pescara, Italy
[3] San Carlo Hosp, Rheumatol Dept Lucania, Potenza, Italy
[4] Madonna Grazie Hosp, Matera, Italy
关键词
Bruton's agammaglobulinemia; Bruton's disease; X-linked agammaglobulinemia; psoriatic arthritis;
D O I
10.1080/03009740310003965
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
We describe a 47-year-old male patient suffering from X-linked (or Bruton's) agammaglobulinemia with severe psoriatic arthritis (PsA), which started in childhood. PsA has been previously described in T-cell defective disorders, such as HIV infection, but our observation demonstrates that this rheumatic disease can also occur in subjects with B-lymphocyte cell functional impairment. Chronic inflammatory (bacterial?) involvement of the bowel could represent a pathogenetic connection between X-linked agammaglobulinemia and PsA.
引用
收藏
页码:309 / 311
页数:3
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