The presence of a restrictive atrial septal defect in hypoplastic left heart syndrome represents a surgical emergency and may negatively affect survival after operation. A neonate with such a disease association, requiring septectomy upon birth developed intractable respiratory failure due to congenital pulmonary lymphangiectasis. The therapeutic implications of this rare pathologic condition an discussed. (C) 1998 by Elsevier Science Inc.
机构:
Wayne State Univ, Childrens Hosp Michigan, Div Cardiol, Detroit, MI 48201 USAWayne State Univ, Childrens Hosp Michigan, Div Cardiol, Detroit, MI 48201 USA
Chintala, K.
Tian, Z.
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Univ Penn, Childrens Hosp Philadelphia, Sch Med, Cardiac Ctr,Fetal Heart Program, Philadelphia, PA 19104 USAWayne State Univ, Childrens Hosp Michigan, Div Cardiol, Detroit, MI 48201 USA
Tian, Z.
Du, W.
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Wayne State Univ, Childrens Hosp Michigan, Childrens Res Ctr, Detroit, MI 48201 USAWayne State Univ, Childrens Hosp Michigan, Div Cardiol, Detroit, MI 48201 USA
Du, W.
Donaghue, D.
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Univ Penn, Childrens Hosp Philadelphia, Sch Med, Cardiac Ctr,Fetal Heart Program, Philadelphia, PA 19104 USAWayne State Univ, Childrens Hosp Michigan, Div Cardiol, Detroit, MI 48201 USA
Donaghue, D.
Rychik, J.
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Univ Penn, Childrens Hosp Philadelphia, Sch Med, Cardiac Ctr,Fetal Heart Program, Philadelphia, PA 19104 USAWayne State Univ, Childrens Hosp Michigan, Div Cardiol, Detroit, MI 48201 USA