The challenges of closing an ileostomy in patients with total intestinal aganglionosis after small bowel transplant

被引:2
|
作者
Jazi, Fereshteh Salimi [1 ]
Sinclair, Tiffany J. [2 ]
Thorson, Chad M. [1 ]
Castillo, Ricardo [3 ]
Bonham, Andrew C. [4 ]
Esquivel, Carlos O. [4 ]
Bruzoni, Matias [1 ]
机构
[1] Stanford Univ, Lucile Packard Childrens, Div Pediat Surg, Dept Surg,Sch Med, 300 Pasteur Dr,Alway Bldg M116,MC 5733, Stanford, CA 94305 USA
[2] Stanford Univ, Dept Surg, Sch Med, 300 Pasteur Dr Rm H3691, Stanford, CA 94306 USA
[3] Stanford Univ, Div Gastroenterol, Lucile Packard Childrens, Sch Med, 300 Pasteur Dr,Alway Bldg M116,MC 5733, Stanford, CA 94305 USA
[4] Stanford Univ, Div Transplant Surg, Sch Med, 300 Pasteur Dr Rm H3691, Stanford, CA 94306 USA
关键词
Total intestinal aganglionosis; Small bowel transplantation; Hirschsprung's disease; TOTAL COLONIC AGANGLIONOSIS; HIRSCHSPRUNG DISEASE; PULL-THROUGH; EXPERIENCE; OUTCOMES; INVOLVEMENT; MANAGEMENT; CHILDREN;
D O I
10.1007/s00383-017-4216-y
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
We present the case of a 14-year-old male with a history of small bowel transplantation for long segment Hirschsprung's disease who underwent Duhamel ileorectal pull-through procedure. In post-transplant, the patient had no restrictions and was not TPN-dependent. To improve his quality of life, he and his family were interested in closing the ileostomy and undergoing pull-through surgery. The complexity of the case includes the presence of an aganglionic rectal segment-a short root of the mesentery due to the small bowel transplant-and significant immunosuppression. At the moment, he is continent, doing well, and has not had any remarkable complications.
引用
收藏
页码:113 / 116
页数:4
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