CHARACTERIZATION OF A GROUP OF 12 PATIENTS WITH MEVALONATE KINASE DEFICIENCY: SYMPTOMS AND TREATMENT WITH IL-1 INHIBITORS

被引:0
|
作者
Kozlova, A. [1 ]
Burlakov, V. [1 ]
Kuzmenko, N. [1 ]
Zimin, S. [2 ]
Varlamova, T. [1 ]
Barabanova, O. [2 ]
Raikina, E. [1 ]
Shcherbina, A. [1 ]
机构
[1] Fed State Budgetary Inst, Natl Sci & Pract Ctr Pediat Hematol Oncol & Immun, Immunol, Moscow, Russia
[2] Childrens Clin Hosp 9, Immunol, Moscow, Russia
关键词
D O I
10.1136/annrheumdis-2017-eular.2238
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
THU0547
引用
收藏
页码:413 / 413
页数:1
相关论文
共 50 条
  • [21] IGG AUTOANTIBODIES TO IL-1 ALPHA IN THE SERUM OF PATIENTS WITH SKIN DISEASES - INCIDENCE, CHARACTERIZATION AND EFFECT ON THE BLOOD CLEARANCE OF IL-1 ALPHA
    DIDIERJEAN, L
    SCHIFFERLI, J
    STEIGER, G
    SAURAT, JH
    CLINICAL RESEARCH, 1990, 38 (02): : A623 - A623
  • [22] IGG AUTOANTIBODIES TO IL-1 ALPHA IN THE SERUM OF PATIENTS WITH SKIN DISEASES - INCIDENCE, CHARACTERIZATION AND EFFECT ON THE BLOOD CLEARANCE OF IL-1 ALPHA
    DIDIERJEAN, L
    SCHIFFERLI, J
    STEIGER, G
    SAURAT, JH
    JOURNAL OF INVESTIGATIVE DERMATOLOGY, 1990, 94 (04) : 575 - 575
  • [23] Infectious adverse effects during treatment with IL-1 inhibitors in patients with systemic juvenile idiopathic arthritis and autoinflammatory diseases
    Laura Fernandez-Silveira
    M Isabel González-Fernández
    Berta López-Montesinos
    Silvia Benito-Costey
    Inmaculada Calvo-Penadés
    Pediatric Rheumatology, 12 (Suppl 1)
  • [24] IL-1β and Statin Treatment in Patients with Myocardial Infarction and Diabetic Cardiomyopathy
    Liberale, Luca
    Carbone, Federico
    Camici, Giovanni G.
    Montecucco, Fabrizio
    JOURNAL OF CLINICAL MEDICINE, 2019, 8 (11)
  • [25] IFNγ in the Treatment of a Patient With IL12Rβ1 Deficiency and BCGosis
    Alangari A, A.
    Al-Zamil, F.
    Al-Mazrou, A.
    Awadallah, S.
    Kambal, A.
    Casanova, J.
    JOURNAL OF ALLERGY AND CLINICAL IMMUNOLOGY, 2010, 125 (02) : AB74 - AB74
  • [26] Genetic characterization of interleukins (IL-1, IL-1, IL-2, IL-4, IL-8, IL-10, IL-12A, IL-12B, IL-15 and IL-18) with relevant biological roles in lagomorphs
    Neves, Fabiana
    Abrantes, Joana
    Almeida, Tereza
    de Matos, Ana Lemos
    Costa, Paulo P.
    Esteves, Pedro J.
    INNATE IMMUNITY, 2015, 21 (08) : 787 - 801
  • [27] INFLUENCE OF CIRCULATING TUMOUR CELLS ON PRODUCTION OF IL-1ALPHA, IL-1β AND IL-12 IN SERA OF PATIENTS WITH THE PRIMARY DIAGNOSIS OF BREAST CANCER BEFORE TREATMENT
    Vilsmaier, T.
    Rack, B.
    Koenig, A.
    Friese, K.
    Janni, W.
    Jeschke, U.
    Weissenbacher, T.
    ANTICANCER RESEARCH, 2014, 34 (11) : 6849 - 6850
  • [28] IL-1 Inhibitors in the Treatment of Monogenic Periodic Fever Syndromes: From the Past to the Future Perspectives
    Malcova, Hana
    Strizova, Zuzana
    Milota, Tomas
    Striz, Ilja
    Sediva, Anna
    Cebecauerova, Dita
    Horvath, Rudolf
    FRONTIERS IN IMMUNOLOGY, 2021, 11
  • [29] A role for IL-1 inhibitors in the treatment of non-alcoholic fatty liver disease (NAFLD)?
    Tilg, Herbert
    Effenberger, Maria
    Adolph, Timon E.
    EXPERT OPINION ON INVESTIGATIONAL DRUGS, 2020, 29 (02) : 103 - 106
  • [30] The IL-1 inhibitor Canakinumab for Familial Mediterranean Fever: The Greek experience in 12 patients
    Laskari K.
    Boura P.
    Dalekos G.N.
    Garyfallos A.
    Karokis D.
    Pikazis D.
    Settas L.
    Skarantavos G.
    Tsitsami E.
    Sfikakis P.P.
    Pediatric Rheumatology, 13 (Suppl 1)