Defective IL-12/IFNγ pathway in Job syndrome of hyper-IgE and recurrent infections.

被引:0
|
作者
Borges, WG
Augustine, NH
Joyner, JL
Hill, HR
机构
[1] Univ Utah, Dept Pathol, Salt Lake City, UT USA
[2] Univ Utah, Dept Pediat, Salt Lake City, UT USA
[3] Univ Utah, Dept Med, Salt Lake City, UT USA
[4] Hosp Base Brasilia, Dept Pediat, Brasilia, DF, Brazil
关键词
D O I
暂无
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
引用
收藏
页码:7A / 7A
页数:1
相关论文
共 50 条
  • [31] IFN-GAMMA-INDEPENDENT SUPPRESSION OF IGE SYNTHESIS BY IL-12
    VEZZIO, N
    GATELY, M
    KINIWA, M
    WU, CY
    DELESPESSE, G
    JOURNAL OF IMMUNOLOGY, 1993, 150 (08): : A61 - A61
  • [32] Recurrent infections and cytokine imbalance in hyper-IgE syndrome are not due to a defect in Toll-like receptor pathways.
    Renner, ED
    Hoffmann, F
    Pawlita, I
    Hornung, V
    Hartl, D
    Albert, M
    Jansson, A
    Endres, S
    Hartmann, G
    Belohradsky, BH
    Rothenfusser, S
    CLINICAL IMMUNOLOGY, 2005, 115 : S235 - S236
  • [33] Defective regulation of IFNγ and IL-12 by endogenous IL-10 in progressive MS
    Balashov, KE
    Comabella, M
    Ohashi, T
    Khoury, SJ
    Weiner, HL
    NEUROLOGY, 2000, 55 (02) : 192 - 198
  • [34] DEFECTIVE IFN-GAMMA PRODUCTION IN HYPER-IGE ATOPIC-DERMATITIS PATIENTS - EVIDENCE FOR AN INTRINSIC ABNORMALITY
    REINHOLD, U
    WEHRMANN, W
    KUKEL, S
    KREYSEL, HW
    JOURNAL OF INVESTIGATIVE DERMATOLOGY, 1989, 93 (04) : 571 - 572
  • [35] Coronary Abnormalities in Hyper-IgE Recurrent Infection Syndrome: Depiction at Coronary MDCT Angiography
    Gharib, Ahmed M.
    Pettigrew, Roderic I.
    Elagha, Abdalla
    Hsu, Amy
    Welch, Pam
    Holland, Steven M.
    Freeman, Alexandra F.
    AMERICAN JOURNAL OF ROENTGENOLOGY, 2009, 193 (06) : W478 - W481
  • [36] RECOMBINANT HUMAN INTERFERON GAMMA ENHANCES NEUTROPHIL CHEMOTAXIS IN PATIENTS WITH HYPER-IGE AND RECURRENT INFECTIONS
    JEPPSON, JD
    SHIGEOKA, AO
    AUGUSTINE, NH
    RICE, MC
    HILL, HR
    CLINICAL RESEARCH, 1989, 37 (01): : A188 - A188
  • [37] Recurrent Malignancies in Autosomal Recessive Hyper-IGE Syndrome with DOCK8 Deficiency
    Suratannon, N.
    van der Burg, M.
    Dalm, V.
    van Gijn, M.
    van Dongen, J. J. M.
    van Biezen, P.
    Lugtenburg, E.
    van Zelm, M. C.
    Driessen, G. J.
    van Hagen, P. M.
    JOURNAL OF CLINICAL IMMUNOLOGY, 2014, 34 : S267 - S267
  • [38] RECOMBINANT HUMAN INTERFERON GAMMA ENHANCES NEUTROPHIL CHEMOTAXIS IN PATIENTS WITH HYPER-IGE AND RECURRENT INFECTIONS
    JEPPSON, JD
    HILL, HR
    PEDIATRIC RESEARCH, 1989, 25 (04) : A164 - A164
  • [39] The IL-12 signal transduction pathway is defective in malignant T-cells in Sezary syndrome
    Fox, FE
    Niu, Z
    Kao, DMF
    Rook, AH
    JOURNAL OF INVESTIGATIVE DERMATOLOGY, 1997, 109 (03) : 486 - 486
  • [40] Recombinant IL-12 attenuates and prevents dissemination of Cryptococcus neoformans pulmonary infections.
    McAllister, KS
    Goodman, RE
    Huffnagle, GH
    McDonald, RA
    Toews, GB
    FASEB JOURNAL, 1996, 10 (06): : 2517 - 2517