Complete bone regeneration in hemophilic pseudotumor of the mandible

被引:7
|
作者
Otsuka, Hiroki [1 ]
Ozeki, Michio [1 ]
Kanda, Kaori [1 ]
Hori, Tomohiro [1 ]
Kawamoto, Norio [1 ]
Saigo, Chiemi [2 ]
Kato, Hiroki [3 ]
Makita, Hiroki [4 ]
Shibata, Toshiyuki [4 ]
Fukao, Toshiyuki [1 ]
机构
[1] Gifu Univ, Grad Sch Med, Dept Pediat, 1-1 Yanagido, Gifu 5011194, Japan
[2] Gifu Univ, Grad Sch Med, Dept Pathol & Translat Res, Gifu, Japan
[3] Gifu Univ, Sch Med, Dept Radiol, Gifu, Japan
[4] Gifu Univ, Grad Sch Med, Dept Oral & Maxillofacial Sci, Gifu, Japan
关键词
bone regeneration; diagnostic imaging; factor VIII; hemophilia; mandible; PATIENT;
D O I
10.1111/ped.12820
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
Hemophilic pseudotumor (HP) is rare, seen in 1-2% of patients with hemophilia, and is extremely uncommon in the mandible. A 6-year-old boy with moderate hemophilia A presented to our hospital with left mandibular swelling. Based on clinical and radiological findings, a tentative diagnosis of HP was made. After factor VIII administration, the lesion was curetted and HP was confirmed on histopathology. The patient was treated with twice-weekly factor VIII until the lesion had completely resolved and bone had regenerated at 1 year. The best treatment for HP is not established; however, appropriate initial treatment and postoperative prophylaxis are effective.
引用
收藏
页码:406 / 408
页数:3
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