Polymers of Z α1-antitrypsin are secreted in cell models of disease

被引：37

作者：

Fra, Annamaria ^{[1
]}

Cosmi, Francesca ^{[2
]}

Ordonez, Adriana ^{[3
]}

Berardelli, Romina ^{[1
]}

Perez, Juan ^{[4
]}

Guadagno, Noemi A. ^{[2
]}

Corda, Luciano ^{[5
]}

Marciniak, Stefan J. ^{[3
]}

Lomas, David A. ^{[6
]}

Miranda, Elena ^{[2
,7
]}

机构：

[1] Univ Brescia, Dept Mol & Translat Med, Viale Europa 11, I-25123 Brescia, Italy

[2] Sapienza Univ Rome, Dept Biol & Biotechnol Charles Darwin, Rome, Italy

[3] Univ Cambridge, Cambridge Inst Med Res, Dept Med, Cambridge, England

[4] Univ Malaga, Dept Cell Biol Genet & Physiol, Malaga, Spain

[5] Spedali Civil Brescia, Div Internal Med, Brescia, Italy

[6] UCL, Wolfson Inst Biomed Res, London, England

[7] Sapienza Univ Rome, Cenci Bolognetti Fdn, Pasteur Inst, Rome, Italy

来源：

EUROPEAN RESPIRATORY JOURNAL | 2016年 / 47卷 / 03期

基金：

英国医学研究理事会;

关键词：

DEFICIENCY; ALPHA-1-ANTITRYPSIN; POLYMERIZATION; MECHANISM;

D O I：

10.1183/13993003.00940-2015

中图分类号：

R56 [呼吸系及胸部疾病];

学科分类号：

摘要：

引用

页码：1005 / 1009

页数：6

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