Polymers of Z α1-antitrypsin are secreted in cell models of disease

被引：37
|
作者：
Fra, Annamaria [1 ]
Cosmi, Francesca [2 ]
Ordonez, Adriana [3 ]
Berardelli, Romina [1 ]
Perez, Juan [4 ]
Guadagno, Noemi A. [2 ]
Corda, Luciano [5 ]
Marciniak, Stefan J. [3 ]
Lomas, David A. [6 ]
Miranda, Elena [2 ,7 ]
机构：
[1] Univ Brescia, Dept Mol & Translat Med, Viale Europa 11, I-25123 Brescia, Italy
[2] Sapienza Univ Rome, Dept Biol & Biotechnol Charles Darwin, Rome, Italy
[3] Univ Cambridge, Cambridge Inst Med Res, Dept Med, Cambridge, England
[4] Univ Malaga, Dept Cell Biol Genet & Physiol, Malaga, Spain
[5] Spedali Civil Brescia, Div Internal Med, Brescia, Italy
[6] UCL, Wolfson Inst Biomed Res, London, England
[7] Sapienza Univ Rome, Cenci Bolognetti Fdn, Pasteur Inst, Rome, Italy
来源：
EUROPEAN RESPIRATORY JOURNAL | 2016年 / 47卷 / 03期
基金：
英国医学研究理事会;
关键词：
DEFICIENCY; ALPHA-1-ANTITRYPSIN; POLYMERIZATION; MECHANISM;
D O I：
10.1183/13993003.00940-2015
中图分类号：
R56 [呼吸系及胸部疾病];
学科分类号：
摘要：
引用
收藏
页码：1005 / 1009
页数：6
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