Pyogenic arthritis, pyoderma gangrenosum, and acne (PAPA) syndrome: differential diagnosis of septic arthritis by regular detection of exceedingly high synovial cell counts

被引:13
|
作者
Loeffler, W. [1 ]
Lohse, P. [2 ]
Weihmayr, T. [3 ]
Widenmayer, W. [3 ]
机构
[1] Rheumatol Nymphenburg, Nymphenburger Str 108a, D-80636 Munich, Germany
[2] Inst Lab Med, Virchowstr 10 C, D-78224 Singen, Germany
[3] Allgemeinmed & Sportmed Nymphenburg, Nymphenburger Str 108a, D-80636 Munich, Germany
关键词
PAPA syndrome; Arthritis; Acne; Pyoderma gangrenosum; PSTPIP1; Autoinflammatory; Corticosteroids; Anakinra; Canakinumab; Il-1; blocking; TNF alpha blocking; Exercise induced; Synovial fluid cell counts; Pyogenic; Septic; PHOSPHATASE-INTERACTING PROTEIN-1; FAMILIAL MEDITERRANEAN FEVER; PSTPIP1 GENE MUTATION; AUTOINFLAMMATORY DISEASES; CLINICAL-EFFICACY; JOINT INFECTIONS; PATIENT; ETANERCEPT; INTERLEUKIN-1; PATHOGENESIS;
D O I
10.1007/s15010-017-0996-1
中图分类号
R51 [传染病];
学科分类号
100401 ;
摘要
Pyogenic arthritis, pyoderma gangrenosum and acne syndrome was diagnosed in a 42-year-old patient, after an unusual persistency of high synovial cell counts had been noticed. Clinical peculiarities and problems with diagnosing septic versus non-septic arthritis are discussed.
引用
收藏
页码:395 / 402
页数:8
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