Late-onset porokeratotic eccrine ostial and dermal duct nevus associated with sensory polyneuropathy and hyperthyroidism

This 66-year-old Iranian gentle man had a one-year history of asymptomatic keratotic papules with a linear distribution on the skin of his right palm near the wrist. On histopathologic examination-cornoid lamella-like parakeratotic columns above eccrine ducts were observed. The acrosyringium was also dilated. The diagnosis was porokeratotic eccrine ostial and dermal duct nevus. The late-onset development of the disease in our patient was interesting to us, because it is considered a congenital hamartoma.