Progressive severe B cell and NK cell deficiency with T cell senescence in adult CD40L deficiency

被引：5
|
作者：
Lougaris, Vassilios [1 ,2 ]
Lanzi, Gaetana [3 ]
Baronio, Manuela [1 ,2 ]
Gazzurelli, Luisa [1 ,2 ]
Vairo, Donatella [3 ]
Lorenzini, Tiziana [1 ,2 ]
Badolato, Raffaele [1 ,2 ]
Notarangelo, Lucia Dora [4 ]
Boschi, Andrea [5 ]
Moratto, Daniele [3 ]
Plebani, Alessandro [1 ,2 ]
机构：
[1] Univ Brescia, ASST Spedali Civili Brescia, Pediat Clin, Piazzale Spedali Civili 1, I-25123 Brescia, Italy
[2] Univ Brescia, ASST Spedali Civili Brescia, Dept Clin & Expt Sci, Inst Mol Med A Nocivelli, Piazzale Spedali Civili 1, I-25123 Brescia, Italy
[3] Univ Brescia, ASST Spedali Civili Brescia, Inst Mol Med A Nocivelli,Dept Mol & Translat Med, Dept Pathol,Lab Genet Disorders Childhood, Brescia, Italy
[4] ASST Spedali Civili Brescia, Pediat Oncohematol, Brescia, Italy
[5] Rimini Hosp, Infect Dis Unit, Rimini, Italy
来源：
CLINICAL IMMUNOLOGY | 2018年 / 190卷
关键词：
CD40 ligand deficiency; B cells; Natural killer (NK) cells; CD4 T cells; T cell senescence; HYPER-IGM SYNDROME; DEFECTIVE EXPRESSION; LIGAND DEFICIENCY; IMMUNODEFICIENCY;
D O I：
10.1016/j.clim.2018.02.008
中图分类号：
R392 [医学免疫学]; Q939.91 [免疫学];
学科分类号：
100102 ;
摘要：
引用
收藏
页码：11 / 14
页数：4
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