Extremely late-onset pulmonary metastasis from uterine PEComa

被引:2
|
作者
Ascione, Andrea [1 ]
Martignoni, Guido [2 ,3 ]
D'Amati, Giulia [1 ]
Della Rocca, Carlo [4 ]
Graziano, Paolo [5 ]
Pernazza, Angelina [4 ]
机构
[1] Sapienza Univ Rome, Dept Radiol Oncol & Pathol Sci, Rome, Italy
[2] Univ Verona, Dept Diagnost & Publ Hlth, Verona, Italy
[3] Pederzoli Hosp, Pathol Unit, Verona, Italy
[4] Polo Pontino Sapienza Univ, Dept Medicosurg Sci & Biotechnol, I-04100 Latina, Italy
[5] Fdn IRCCS Casa Sollievo Sofferenza, Unit Pathol, Foggia, Italy
关键词
PEComa; soft tissues; uterus; lung; metastases;
D O I
10.32074/1591-951X-762
中图分类号
R36 [病理学];
学科分类号
100104 ;
摘要
A 79-year-old woman underwent surgical resection of a peripheral, solitary, pulmonary lesion that was diagnosed as malignant PEComa. Her clinical history was positive for uterine leiomyosarcoma, excised 20 years before. Re-evaluation of the primary uterine lesion led to the final diagnosis of lung metastasis from uterine PEComa. While long latency between primary tumour and metastasis is a known and characteristic feature of PEComas, a 20-year interval is unprecedented in the literature.
引用
收藏
页码:312 / 315
页数:4
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