Airway Clearance Techniques for Primary Ciliary Dyskinesia; is the Cystic Fibrosis literature portable?

被引:17
|
作者
Schofield, Lynne Marie [1 ]
Duff, Alistair [1 ]
Brennan, Cathy [2 ]
机构
[1] Leeds Gen Infirm, Leeds Teaching Hosp, Great George St, Leeds LS1 3EX, W Yorkshire, England
[2] Univ Leeds, Leeds Inst Hlth Sci, Leeds, W Yorkshire, England
关键词
PCD; Chest Physiotherapy; Airway Clearance; CF; KARTAGENERS-SYNDROME; EUROPEAN CHILDREN; PHYSIOTHERAPY; RECOMMENDATIONS; MANAGEMENT; CONSENSUS; INFANTS; QUALITY; COHORT; DNASE;
D O I
10.1016/j.prrv.2017.03.011
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
Primary Ciliary Dyskinesia (PCD) is a rare inherited disease with impaired mucociliary clearance. Airway clearance techniques (ACTs) are commonly recommended for patients with PCD to facilitate mucus clearance, despite a lack of evidence in this group. Current physiotherapy practice in PCD is based on evidence extrapolated from the field of Cystic Fibrosis (CF). This paper focuses on the available evidence and outlines challenges in extrapolating evidence between the conditions for best clinical practice. (C) 2017 Published by Elsevier Ltd.
引用
下载
收藏
页码:73 / 77
页数:5
相关论文
共 50 条
  • [31] Psychological status of mothers of children with cystic fibrosis and primary ciliary dyskinesia
    Gursoy, Tugba Ramasli
    Eyuboglu, Tugba Sismanlar
    Aslan, Ayse T.
    Emiralioglu, Nagehan
    Pekcan, Sevgi
    Buyukkaya, Eda Z.
    Hangul, Melih
    Kose, Mehmet
    Soysal, Sebnem
    Budakoglu, Isil I.
    PEDIATRIC PULMONOLOGY, 2022, 57 (11) : 2665 - 2673
  • [32] Comparison of bronchodilator responsiveness in children with primary ciliary dyskinesia and cystic fibrosis
    Keenan, Victoria
    Harris, Amanda
    Payne, Sarah
    Yonge, Caroline
    Rubbo, Bruna
    Friend, Amanda
    Gove, Kerry
    Legg, Julian
    Evans, Hazel
    Jane, Lucas
    Gary, Connett
    Woolf, Walker
    EUROPEAN RESPIRATORY JOURNAL, 2016, 48
  • [33] Bacterial infections in patients with primary ciliary dyskinesia: Comparison with cystic fibrosis
    Wijers, Christiaan D. M.
    Chmiel, James F.
    Gaston, Benjamin M.
    CHRONIC RESPIRATORY DISEASE, 2017, 14 (04) : 392 - 406
  • [34] A novel, noninvasive assay shows that distal airway oxygen tension is low in cystic fibrosis, but not in primary ciliary dyskinesia
    Mendelsohn, Lori
    Wijers, Christiaan
    Gupta, Ritika
    Marozkina, Nadzeya
    Li, Chun
    Gaston, Benjamin
    PEDIATRIC PULMONOLOGY, 2019, 54 (01) : 27 - 32
  • [35] Finding evidence to support airway clearance techniques in cystic fibrosis
    Prasad, SA
    Main, E
    DISABILITY AND REHABILITATION, 1998, 20 (6-7) : 235 - 246
  • [36] A systematic review of lung clearance index in non-cystic fibrosis, non-primary ciliary dyskinesia bronchiectasis
    Hine, Christopher
    Desai, Maya
    Davies, Jane
    Sapey, Elizabeth
    Nagakumar, Prasad
    RESPIRATORY MEDICINE, 2022, 201
  • [37] Incentive techniques and airway clearance, therapy in teenagers with cystic fibrosis
    Almajan-Guta, B.
    Avram, C.
    Rusu, A. M.
    Filipescu, H.
    Almajan-Guta, V.
    Cluci, O.
    Pop, L.
    Oravitan, M.
    6TH WORLD CONGRESS OF THE INTERNATIONAL SOCIETY OF PHYSICAL AND REHABILITATION MEDICINE, 2011, : 42 - +
  • [38] Airway clearance techniques used by people with cystic fibrosis in the UK
    Hoo, Z. H.
    Daniels, T.
    Wildman, M. J.
    Teare, M. D.
    Bradley, J. M.
    PHYSIOTHERAPY, 2015, 101 (04) : 340 - 348
  • [39] Airway clearance techniques in cystic fibrosis: physiology, devices and the future
    Kendrick, Adrian H.
    JOURNAL OF THE ROYAL SOCIETY OF MEDICINE, 2007, 100 : 3 - 23
  • [40] Exercise versus airway clearance techniques for people with cystic fibrosis
    Heinz, Katie D.
    Walsh, Adam
    Southern, Kevin W.
    Johnstone, Zoe
    Regan, Kate H.
    COCHRANE DATABASE OF SYSTEMATIC REVIEWS, 2022, (06):