Airway Clearance Techniques for Primary Ciliary Dyskinesia; is the Cystic Fibrosis literature portable?

被引:17
|
作者
Schofield, Lynne Marie [1 ]
Duff, Alistair [1 ]
Brennan, Cathy [2 ]
机构
[1] Leeds Gen Infirm, Leeds Teaching Hosp, Great George St, Leeds LS1 3EX, W Yorkshire, England
[2] Univ Leeds, Leeds Inst Hlth Sci, Leeds, W Yorkshire, England
关键词
PCD; Chest Physiotherapy; Airway Clearance; CF; KARTAGENERS-SYNDROME; EUROPEAN CHILDREN; PHYSIOTHERAPY; RECOMMENDATIONS; MANAGEMENT; CONSENSUS; INFANTS; QUALITY; COHORT; DNASE;
D O I
10.1016/j.prrv.2017.03.011
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
Primary Ciliary Dyskinesia (PCD) is a rare inherited disease with impaired mucociliary clearance. Airway clearance techniques (ACTs) are commonly recommended for patients with PCD to facilitate mucus clearance, despite a lack of evidence in this group. Current physiotherapy practice in PCD is based on evidence extrapolated from the field of Cystic Fibrosis (CF). This paper focuses on the available evidence and outlines challenges in extrapolating evidence between the conditions for best clinical practice. (C) 2017 Published by Elsevier Ltd.
引用
下载
收藏
页码:73 / 77
页数:5
相关论文
共 50 条
  • [1] Airway clearance techniques compared to no airway clearance techniques for cystic fibrosis
    Warnock, Louise
    Gates, Alison
    COCHRANE DATABASE OF SYSTEMATIC REVIEWS, 2023, (04):
  • [2] Comparison of the Lung Clearance Index in Preschool Children With Primary Ciliary Dyskinesia and Cystic Fibrosis
    Roehmel, Jobst F.
    Doerfler, Friederike J.
    Koerner-Rettberg, Cordula
    Brinkmann, Folke
    Schlegtendal, Anne
    Wetzke, Martin
    Rudolf, Isa
    Helms, Simone
    Grosse-Onnebrink, Joerg
    Yu, Yin
    Nuesslein, Thomas
    Wojsyk-Banaszak, Irena
    Becker, Sebastian
    Eickmeier, Olaf
    Sommerburg, Olaf
    Omran, Heymut
    Stahl, Mirjam
    Mall, Marcus A.
    CHEST, 2022, 162 (03) : 534 - 542
  • [3] Comparison of the Lung Clearance Index in preschool children with Primary Ciliary Dyskinesia and Cystic Fibrosis
    Roehmel, J.
    Doerfler, F.
    Koerner-Rettberg, C.
    Brinkmann, F.
    Schlegtendal, A.
    Wetzke, M.
    Rudolf, I
    Helms, S.
    Grosse-Onnebrink, J.
    Yu, Y.
    Nuesslein, T.
    Wojsyk-Banaszak, I
    Becker, S.
    Eickmeier, O.
    Sommerburg, O.
    Omran, H.
    Stahl, M.
    Mall, M.
    KLINISCHE PADIATRIE, 2022, 234 (05): : 335 - 335
  • [4] Comparison of the lung clearance index in preschool children with primary ciliary dyskinesia and cystic fibrosis
    Roehmel, J.
    Doerfler, F.
    Koerner-Rettberg, C.
    Brinkmann, F.
    Schlegtendal, A.
    Wetzke, M.
    Rudolf, I
    Helms, S.
    Grosse-Onnebrink, J.
    Yu, Y.
    Nuesslein, T.
    Wojsyk-Banaszak, I
    Becker, S.
    Eickmeier, O.
    Sommerburg, O.
    Omran, H.
    Stahl, M.
    Mall, M.
    EUROPEAN RESPIRATORY JOURNAL, 2022, 60
  • [5] Airway clearance techniques in cystic fibrosis
    Kendrick, AH
    EUROPEAN RESPIRATORY JOURNAL, 2006, 27 (06) : 1082 - 1083
  • [6] Prolonged airway retention of insoluble particles in cystic fibrosis versus primary ciliary dyskinesia
    Regnis, JA
    Zeman, KL
    Noone, PG
    Knowles, RR
    Bennett, WD
    EXPERIMENTAL LUNG RESEARCH, 2000, 26 (03) : 149 - 162
  • [7] Cystic fibrosis and primary ciliary dyskinesia: Similarities and differences
    Pereira, Rute
    Barbosa, Telma
    Cardoso, Ana Lucia
    Sa, Rosalia
    Sousa, Mario
    RESPIRATORY MEDICINE, 2023, 209
  • [8] LUNG CLEARANCE INDEX AND STRUCTURAL LUNG DISEASE IN CYSTIC FIBROSIS: A COMPARISON WITH PRIMARY CILIARY DYSKINESIA
    Ives, A.
    Irving, S.
    Hogg, C.
    Edey, A.
    Hansell, D.
    Alton, E. W.
    Davies, J. C.
    Bush, A.
    PEDIATRIC PULMONOLOGY, 2010, : 361 - 362
  • [9] Changes in airway inflammation during pulmonary exacerbations in patients with cystic fibrosis and primary ciliary dyskinesia
    Ratjen, Felix
    Waters, Valerie
    Klingel, Michelle
    McDonald, Nancy
    Dell, Sharon
    Leahy, Timothy Ronan
    Yau, Yvonne
    Grasemann, Hartmut
    EUROPEAN RESPIRATORY JOURNAL, 2016, 47 (03) : 829 - 836
  • [10] Upper and lower airway nitric oxide levels in primary ciliary dyskinesia, cystic fibrosis and asthma
    Walker, W. T.
    Liew, A.
    Harris, A.
    Cole, J.
    Lucas, J. S.
    RESPIRATORY MEDICINE, 2013, 107 (03) : 380 - 386