We report a rare patient with an intrasphenoidal Rathke's cleft cyst (RCC) and review the literature. RCC are benign epithelium lined cysts containing mucoid material, which typically occur in a location that is either entirely intrasellar, or intrasellar with suprasellar extension (intra-suprasellar). RCC in a completely extrasellar location are uncommon. An intrasphenoidal RCC is extremely rare with only two patients reported in the literature to date. Preoperative diagnosis is difficult due to the uncommon location and absence of any characteristic radiological features. However, it remains of utmost clinical relevance because it may limit the operative management to biopsy sampling of the cyst wall and drainage of the contents via the transsphenoidal route. (C) 2015 Elsevier Ltd. All rights reserved.
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Ankara Etlik City Hosp, Pediat Endocrinol Clin, Ankara, TurkiyeAnkara Etlik City Hosp, Pediat Endocrinol Clin, Ankara, Turkiye
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Ankara Etlik City Hosp, Pediat Endocrinol Clin, Ankara, Turkiye
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Ankara Etlik City Hosp, Pediat Endocrinol Clin, Ankara, Turkiye
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HORMONE RESEARCH IN PAEDIATRICS,
2024,
97
: 629
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629
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Yonsei Univ, Coll Med, Dept Neurosurg, Brain Res Inst, Seoul 120752, South KoreaYonsei Univ, Coll Med, Dept Neurosurg, Brain Res Inst, Seoul 120752, South Korea
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Yonsei Univ, Coll Med, Dept Neurosurg, Brain Res Inst, Seoul 120752, South KoreaYonsei Univ, Coll Med, Dept Neurosurg, Brain Res Inst, Seoul 120752, South Korea
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Nippon Vet & Life Sci Univ, Dept Vet Sci, Div Vet Radiol, Tokyo 1808602, JapanNippon Vet & Life Sci Univ, Dept Vet Sci, Div Vet Radiol, Tokyo 1808602, Japan
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