Dominant optic atrophy caused by a novel OPA1 mutation:: Disruption of the mitochondrial network with preserved bioenergetics

被引:0
|
作者
Spinazzi, Marco [1 ]
Cazzola, Silvia [1 ]
Bortolozzi, Mario [2 ]
Baracca, Alessandra [3 ]
Loro, Emanuele [1 ]
Solaini, Giancarlo [3 ]
Sgarbi, Gianluca [3 ]
Cenacchi, Giovanna [4 ]
Malena, Adriana [1 ]
Scorrano, Luca [5 ]
Frezza, Christian [5 ]
Angelini, Corrado [1 ]
Vergani, Lodovica [1 ]
机构
[1] Univ Padua, Dept Neurosci, I-35100 Padua, Italy
[2] Mol Med, Padua, Italy
[3] Univ Bologna, Dept Biochem, I-40126 Bologna, Italy
[4] Univ Bologna, Dept Radiol Histocytopathol Sci, I-40126 Bologna, Italy
[5] Dulbecco Telethon Inst, Padua, Italy
关键词
D O I
10.1016/j.bbabio.2008.05.222
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
引用
收藏
页码:S56 / S56
页数:1
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