Kikuchi-Fujimoto disease (KFD) is a benign and self-limited disease of unknown etiology that affects mainly young women. It presents with localized lymphadenopathy, usually cervical, accompanied with fever, night sweats, and leucopenia. KFD has been rarely described in association with autoimmune disorders, mainly systemic lupus erythematosus (SLE). We report the case of a young patient presenting with KFD coinciding with SLE. The association of KFD and SLE is reviewed. Moreover, a possible pathogenetic role of Ebstein-Barr virus linking the two clinical entities is discussed.
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Univ Indonesia, Dr Cipto Mangunkusumo Hosp, Dept Child Hlth, Fac Med, Jakarta, IndonesiaUniv Indonesia, Dr Cipto Mangunkusumo Hosp, Dept Child Hlth, Fac Med, Jakarta, Indonesia
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Gulhane Askeri Tip Akad, Infeksiyon & Hastakklari Klin, Mikrobiyol Anabilim Dali, Ankara, TurkeyGulhane Askeri Tip Akad, Infeksiyon & Hastakklari Klin, Mikrobiyol Anabilim Dali, Ankara, Turkey
Beker, Can Murat
Dizer, Ufuk
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Gulhane Askeri Tip Akad, Infeksiyon & Hastakklari Klin, Mikrobiyol Anabilim Dali, Ankara, TurkeyGulhane Askeri Tip Akad, Infeksiyon & Hastakklari Klin, Mikrobiyol Anabilim Dali, Ankara, Turkey
Dizer, Ufuk
Ikiz, Saner
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Gulhane Askeri Tip Akad, Infeksiyon & Hastakklari Klin, Mikrobiyol Anabilim Dali, Ankara, TurkeyGulhane Askeri Tip Akad, Infeksiyon & Hastakklari Klin, Mikrobiyol Anabilim Dali, Ankara, Turkey
Ikiz, Saner
Gorenek, Levent
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Gulhane Askeri Tip Akad, Infeksiyon & Hastakklari Klin, Mikrobiyol Anabilim Dali, Ankara, TurkeyGulhane Askeri Tip Akad, Infeksiyon & Hastakklari Klin, Mikrobiyol Anabilim Dali, Ankara, Turkey
Gorenek, Levent
Pahsa, Alaaddin
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Gulhane Askeri Tip Akad, Infeksiyon & Hastakklari Klin, Mikrobiyol Anabilim Dali, Ankara, TurkeyGulhane Askeri Tip Akad, Infeksiyon & Hastakklari Klin, Mikrobiyol Anabilim Dali, Ankara, Turkey