Aetiology and epidemiology of primary lymphoedema:: review

被引:7
|
作者
Kröll, A [1 ]
Neuhüttler, S [1 ]
Brenner, E [1 ]
机构
[1] Univ Innsbruck, Div Klin Funktionelle Anat, Dept Anat Histol & Embryol, A-6020 Innsbruck, Austria
关键词
lymphoedema;
D O I
10.1055/s-0037-1622124
中图分类号
R6 [外科学];
学科分类号
1002 ; 100210 ;
摘要
A considerable number of patients suffer from genetically caused primary lymphoedema. Nevertheless, sound epidemiological data are sparse. This review summons the current knowledge on the genetic reasons and foundations. The review covers the following diseases and syndromes: Klippel-Tienaunay, Nonne-Milroy, Waver and Sotos, Lissencephalia (Norman-Roberts-Type), Buschke-Ollendorff, Noonan, Aagenaes, Meige, Lymphoedema-Distichiasis, Yellow-Nail, Lymphoedemo and Ptosis, Hypotrichosis-Lymphedemo-Teleangiectasia, Konzaki-Disease, Lymphoedema-Microcepholy (-Chorioretinopothy), unilateral Giant Breast, Hennekam, congenital recessive lymphoedema, Aarskog-S(on, OLEDAID, Lymphoedema-Hypopofathyrecidism, Campomelia (Cumming-Type), and Swyer.
引用
收藏
页码:3 / 10
页数:8
相关论文
共 50 条
  • [31] CONTRIBUTIONS TO AETIOLOGY AND EPIDEMIOLOGY OF SALMONELLOSES
    MARGORINA, L
    SHATROV, II
    TYUTKINA, NF
    BILIBIN, AF
    JOURNAL OF MICROBIOLOGY EPIDEMIOLOGY AND IMMUNOBIOLOGY USSR, 1961, 32 (02): : 281 - &
  • [32] The aetiology and epidemiology of faecal incontinence
    Francombe, J
    Carter, S
    Hershman, MJ
    HOSPITAL MEDICINE, 2001, 62 (09): : 529 - 532
  • [33] The Epidemiology and Aetiology of Injuries in Sailing
    Vernon Neville
    Jonathan P. Folland
    Sports Medicine, 2009, 39 : 129 - 145
  • [34] Aetiology and epidemiology of bovine paratuberculosis
    Douart, A
    Maillard, R
    POINT VETERINAIRE, 2001, 32 (219): : 38 - +
  • [35] The Epidemiology and Aetiology of Injuries in Sailing
    Neville, Vernon
    Folland, Jonathan P.
    SPORTS MEDICINE, 2009, 39 (02) : 129 - 145
  • [36] 2 CASES OF PRIMARY LYMPHOEDEMA
    BORRIE, PF
    PROCEEDINGS OF THE ROYAL SOCIETY OF MEDICINE-LONDON, 1960, 53 (05): : 382 - 383
  • [37] PRIMARY LYMPHOEDEMA OF LOWER LIMB
    KINMONTH, JB
    PROCEEDINGS OF THE ROYAL SOCIETY OF MEDICINE-LONDON, 1965, 58 (12): : 1021 - +
  • [38] Immune dysfunction in primary lymphoedema
    Pearce, J.
    Mortimer, P.
    Mansour, S.
    Gordon, K.
    Macallan, D.
    BRITISH JOURNAL OF DERMATOLOGY, 2021, 185 : 146 - 146
  • [39] CHYLOUS COMPLICATIONS OF PRIMARY LYMPHOEDEMA
    KINMONTH, JB
    JANTET, GH
    TAYLOR, GW
    JOURNAL OF CARDIOVASCULAR SURGERY, 1964, 5 (04): : 327 - +
  • [40] DIURETIC THERAPY OF PRIMARY LYMPHOEDEMA
    CATTELL, WR
    TAYLOR, GW
    AITKEN, D
    LANCET, 1965, 2 (7407): : 312 - &