Tracheobronchial stent insertions in the management of major airway obstruction in a patient with Hunter syndrome (type-II mucopolysaccharidosis)

被引：10
|
作者：
Davitt, SM
Hatrick, A
Sabharwal, T
Pearce, A
Gleeson, M
Adam, A
机构：
[1] Guys & St Thomas Hosp, Dept Radiol, London SE1 9RT, England
[2] Guys & St Thomas Hosp, Dept Otolaryngol, London SE1 9RT, England
来源：
EUROPEAN RADIOLOGY | 2002年 / 12卷 / 02期
关键词：
mucopolysaccharidoses; airway obstruction; stents; interventional radiology;
D O I：
10.1007/s003300100932
中图分类号：
R8 [特种医学]; R445 [影像诊断学];
学科分类号：
1002 ; 100207 ; 1009 ;
摘要：
We report a case of a 22-year-old male with Hunter syndrome who developed progressive major airway obstruction and was treated with insertion of plastic and metallic stents. with dramatic improvement in the patient's symptomatic and functional status. To the best of our knowledge, this is the first reported case of endoluminal stents being used in the management of major airway obstruction in a patient with Hunter syndrome.
引用
收藏
页码：458 / 462
页数：5
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