Pulmonary hypertension in POEMS syndrome: resolution following radiotherapy

被引：2
|
作者：
Brewis, Melanie J. [1 ]
Church, Alistair C. [1 ]
Peacock, Andrew J. [1 ]
Thomson, Stephen [1 ]
Tighe, Jane [2 ]
Johnson, Martin K. [1 ]
机构：
[1] Golden Jubilee Natl Hosp, Scottish Pulm Vasc Unit, Level 1,Agamemnon St, Glasgow G81 4DY, Lanark, Scotland
[2] Aberdeen Royal Infirm, Dept Haematol, Aberdeen, Scotland
来源：
PULMONARY CIRCULATION | 2014年 / 4卷 / 04期
关键词：
plasmacytoma; sildenafil; bosentan;
D O I：
10.1086/678553
中图分类号：
R5 [内科学];
学科分类号：
1002 ; 100201 ;
摘要：
Pulmonary hypertension (PH) is defined by the presence of a mean pulmonary artery pressure (mPAP) >= 25 mmHg. It may be idiopathic or arise as a consequence of a number of diverse conditions. PH has been reported in association with POEMS syndrome (polyneuropathy, organomegaly, endocrinopathy, monoclonal plasma cell disorder, and skin changes), with reversal following systemic treatment with corticosteroids. We report a case of pulmonary hypertension associated with POEMS syndrome treated with radical radiotherapy locally to bone lesions with resolution of systemic disease.
引用
收藏
页码：732 / 735
页数：4
相关论文
共 50 条
  • [21] YELLOW NAIL SYNDROME RESOLUTION FOLLOWING TREATMENT OF PULMONARY TUBERCULOSIS
    PANG, SM
    INTERNATIONAL JOURNAL OF DERMATOLOGY, 1993, 32 (08) : 605 - 606
  • [22] Systemic corticosteroids as first-line treatment in pulmonary hypertension associated with POEMS syndrome
    Rached, Samia
    Athanazio, Rodrigo Abensur
    Dias Junior, Servulo Azevedo
    Jardim, Carlos
    Souza, Rogerio
    JORNAL BRASILEIRO DE PNEUMOLOGIA, 2009, 35 (08) : 804 - 808
  • [23] Soluble immune mediators in POEMS syndrome with pulmonary hypertension: Case report and review of the literature
    Feinberg, L
    Temple, D
    de Marchena, E
    Patarca, R
    Mitrani, A
    CRITICAL REVIEWS IN ONCOGENESIS, 1999, 10 (04): : 293 - 302
  • [24] AN ATYPICAL PULMONARY MANIFESTATION OF POEMS SYNDROME
    Alexander, Krystal
    Abu Sayf, Alaa
    CHEST, 2022, 162 (04) : 2234A - 2235A
  • [25] Sildenafil and steroid therapy effectively improved POEMS syndrome-associated pulmonary arterial hypertension
    Yoshimitsu Shimomura
    Masahiko Hara
    Isamu Mizote
    Yoshikazu Nakaoka
    Hirokazu Tanaka
    Yoshihiro Asano
    Yasushi Sakata
    Issei Komuro
    International Journal of Hematology, 2010, 92 : 774 - 776
  • [26] Severe Pulmonary Hypertension Caused by Smoldering Plasma Cell Myeloma: An Autopsy Case of POEMS Syndrome
    Chinen, Katsuya
    Fujioka, Yasunori
    CASE REPORTS IN MEDICINE, 2012, 2012
  • [27] Sildenafil and steroid therapy effectively improved POEMS syndrome-associated pulmonary arterial hypertension
    Shimomura, Yoshimitsu
    Hara, Masahiko
    Mizote, Isamu
    Nakaoka, Yoshikazu
    Tanaka, Hirokazu
    Asano, Yoshihiro
    Sakata, Yasushi
    Komuro, Issei
    INTERNATIONAL JOURNAL OF HEMATOLOGY, 2010, 92 (05) : 774 - 776
  • [28] A case of non-cardiogenic acute pulmonary edema in a patient with POEMS syndrome-associated pulmonary arterial hypertension
    Masahiko Hara
    Isamu Mizote
    Yoshikazu Nakaoka
    Hirokazu Tanaka
    Yoshihiro Asano
    Yasushi Sakata
    Issei Komuro
    Annals of Hematology, 2011, 90 : 489 - 490
  • [29] A case of non-cardiogenic acute pulmonary edema in a patient with POEMS syndrome-associated pulmonary arterial hypertension
    Hara, Masahiko
    Mizote, Isamu
    Nakaoka, Yoshikazu
    Tanaka, Hirokazu
    Asano, Yoshihiro
    Sakata, Yasushi
    Komuro, Issei
    ANNALS OF HEMATOLOGY, 2011, 90 (04) : 489 - 490
  • [30] Resolution Of Severe pulmonary Hypertension And Right Ventricular Failure In A Patient With Antiphospholipid Antibody Syndrome And Suspected Chronic Thromboembolic Pulmonary Hypertension
    Bevill, B. T.
    Argula, R. G.
    Strange, C. B.
    Gilkeson, G.
    Kim, N. H.
    AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE, 2016, 193
12345