Orthotopic liver transplantation for polycystic liver disease with massive hepatomegaly

History: A 51-year-old man (126kg, 192cm) with massive hepatomegaly causing cardiopulmonary symptoms was referred to our transplant center 14 years after initial diagnosis of polycystic liver disease. Treatment and course: Uneventful hepatectomy was followed by orthotopic liver transplantation using caval replacement. Donor liver came from a 73-year-old woman (extended criteria donor organ offer). A portocaval shunting was not established during transplantation although the explanted liver weighed 22kg. 18 months after transplantation liver function is stable and the patient enjoys normal quality of life. Conclusion: This case report demonstrates the value and success of transplantation for patients suffering from enormous hepatomegaly due to polycystic liver disease.