Juvenile hyaline fibromatosis of gingiva: A case report

被引:15
|
作者
Piattelli, A
Scarano, A
DiBellucci, A
Matarasso, S
机构
[1] UNIV CHIETI,SCH DENT,DEPT ORAL MED & PATHOL,CHIETI,ITALY
[2] SANTOBONO HOSP,DEPT DENT,NAPLES,ITALY
[3] UNIV NAPLES,SCH DENT,DEPT PERIODONTOL,I-80138 NAPLES,ITALY
关键词
fibromatosis; juvenile hyaline; metabolism; inborn errors;
D O I
10.1902/jop.1996.67.4.451
中图分类号
R78 [口腔科学];
学科分类号
1003 ;
摘要
JUVENILE HYALINE FIBROMATOSIS is an extremely rare inherited condition, probably resulting from an inborn error of metabolism. It is characterized by cutaneous nodules, gingival hypertrophy and joint contractions. It affects children but usually it is not present at birth, and is microscopically characterized by a conspicuous hyalinization of the connective tissue.
引用
收藏
页码:451 / 453
页数:3
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