Cognitive abilities in Williams syndrome

被引：17

作者：

Miezah, Daniel ^{[1
]}

Porter, Melanie ^{[1
]}

Batchelor, Jennifer ^{[1
]}

Boulton, Kelsie ^{[1
]}

Veloso, Gabrielle Campos ^{[1
]}

机构：

[1] Macquarie Univ, Psychol Dept, Herring Rd, Sydney, NSW 2109, Australia

来源：

RESEARCH IN DEVELOPMENTAL DISABILITIES | 2020年 / 104卷

关键词：

Williams syndrome; Cognitive abilities; Cognitive heterogeneity; Cognitive homogeneity; BEUREN-SYNDROME; DOWN-SYNDROME; PHENOTYPE; CHILDREN; HETEROGENEITY; INDIVIDUALS; STRENGTHS; ADULTS; SKILLS;

D O I：

10.1016/j.ridd.2020.103701

中图分类号：

G76 [特殊教育];

学科分类号：

040109 ;

摘要：

The current study utilized a comprehensive neuropsychological test battery to investigate cognitive abilities in a sample of 49 WS individuals (25 male) aged 6-39 years. Age effects were also investigated by splitting the sample into child and adult groups. Cognitive heterogeneity was found on the Woodcock Johnson III Tests of Cognitive Abilities, Australian Adaptation (WJ-III COG) (Woodcock, McGrew, & Mather, 2001), with cognitive abilities ranging from profoundly impaired to superior and individualized profiles of strength and weakness varying considerably. Overall, findings supported previous research showing strengths in auditory processing and phonemic awareness. The weakest performance, on average, was in processing speed, attention, delayed associative learning and executive functioning capabilities. Visual-spatial functioning was not a weakness overall, neither was nonverbal reasoning. Chronological age did not relate significantly to cognitive abilities. Findings highlight the need for individual assessment and management of WS individuals.

引用

页数：13

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