In this report the authors describe a unique case of spinal clear cell meningioma in a 13-year-old girl. Clear cell meningiomas (CCMs) are not uncommon. To the authors' knowledge, 14 cases of pediatric CCM occurring in the spinal canal have been reported. Factors lending resistance to meningioma initiation and invasion are analyzed. This 13-year-old girl presented with pain radiating down her left leg. Admission MR imaging showed an inhomogeneous enhancing intradural-extramedullary mass at the L4-5 level. Resection revealed a CCM, and radiotherapy was subsequently administered. Postoperatively there has been no recurrence in > 2 years. In this paper the authors report a case of CCM and provide a comprehensive literature review on this disease. Current recommendations for its management are still debatable, especially in the pediatric population, and the authors propose an algorithm for its treatment and surveillance. (DOI: 10.3171/2008.10.17668)
机构:
Sun Yat Sen Univ, Affiliated Hosp 1, Dept Pathol, Guangzhou 510080, Guangdong, Peoples R ChinaSun Yat Sen Univ, Affiliated Hosp 1, Dept Pathol, Guangzhou 510080, Guangdong, Peoples R China
Wu Tong-tong
Bian Li-juan
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Sun Yat Sen Univ, Affiliated Hosp 2, Dept Pathol, Guangzhou 510080, Guangdong, Peoples R ChinaSun Yat Sen Univ, Affiliated Hosp 1, Dept Pathol, Guangzhou 510080, Guangdong, Peoples R China
Bian Li-juan
Li Zhi
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Sun Yat Sen Univ, Affiliated Hosp 1, Dept Pathol, Guangzhou 510080, Guangdong, Peoples R ChinaSun Yat Sen Univ, Affiliated Hosp 1, Dept Pathol, Guangzhou 510080, Guangdong, Peoples R China
Li Zhi
Li Yang
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Sun Yat Sen Univ, Affiliated Hosp 1, Dept Pathol, Guangzhou 510080, Guangdong, Peoples R ChinaSun Yat Sen Univ, Affiliated Hosp 1, Dept Pathol, Guangzhou 510080, Guangdong, Peoples R China
Li Yang
Luo Bo-ning
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Sun Yat Sen Univ, Affiliated Hosp 1, Dept Radiol, Guangzhou 510080, Guangdong, Peoples R ChinaSun Yat Sen Univ, Affiliated Hosp 1, Dept Pathol, Guangzhou 510080, Guangdong, Peoples R China
Luo Bo-ning
Huang Quan
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Sun Yat Sen Univ, Affiliated Hosp 1, Dept Neurosurg, Guangzhou 510080, Guangdong, Peoples R ChinaSun Yat Sen Univ, Affiliated Hosp 1, Dept Pathol, Guangzhou 510080, Guangdong, Peoples R China
机构:
Univ Yamanashi, Interdisciplinary Grad Sch Med & Engn, Dept Neurosurg, Chuo Ku, Yamanashi 4093898, JapanUniv Yamanashi, Interdisciplinary Grad Sch Med & Engn, Dept Neurosurg, Chuo Ku, Yamanashi 4093898, Japan
Sato, Takashi
Sugiyama, Takeshi
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Univ Yamanashi, Interdisciplinary Grad Sch Med & Engn, Dept Pediat, Chuo Ku, Yamanashi 4093898, JapanUniv Yamanashi, Interdisciplinary Grad Sch Med & Engn, Dept Neurosurg, Chuo Ku, Yamanashi 4093898, Japan
Sugiyama, Takeshi
Kawataki, Tomoyuki
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Univ Yamanashi, Interdisciplinary Grad Sch Med & Engn, Dept Neurosurg, Chuo Ku, Yamanashi 4093898, JapanUniv Yamanashi, Interdisciplinary Grad Sch Med & Engn, Dept Neurosurg, Chuo Ku, Yamanashi 4093898, Japan
Kawataki, Tomoyuki
Sato, Eiji
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Univ Yamanashi, Interdisciplinary Grad Sch Med & Engn, Dept Neurosurg, Chuo Ku, Yamanashi 4093898, JapanUniv Yamanashi, Interdisciplinary Grad Sch Med & Engn, Dept Neurosurg, Chuo Ku, Yamanashi 4093898, Japan
Sato, Eiji
Horikoshi, Toru
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Univ Yamanashi, Interdisciplinary Grad Sch Med & Engn, Dept Neurosurg, Chuo Ku, Yamanashi 4093898, JapanUniv Yamanashi, Interdisciplinary Grad Sch Med & Engn, Dept Neurosurg, Chuo Ku, Yamanashi 4093898, Japan
Horikoshi, Toru
Sugita, Kanji
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Univ Yamanashi, Interdisciplinary Grad Sch Med & Engn, Dept Pediat, Chuo Ku, Yamanashi 4093898, JapanUniv Yamanashi, Interdisciplinary Grad Sch Med & Engn, Dept Neurosurg, Chuo Ku, Yamanashi 4093898, Japan
Sugita, Kanji
Kinouchi, Hiroyuki
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Univ Yamanashi, Interdisciplinary Grad Sch Med & Engn, Dept Neurosurg, Chuo Ku, Yamanashi 4093898, JapanUniv Yamanashi, Interdisciplinary Grad Sch Med & Engn, Dept Neurosurg, Chuo Ku, Yamanashi 4093898, Japan
机构:
Univ Campinas Unicamp, Dept Pathol, Fac Med Sci, BR-13083970 Campinas, SP, BrazilUniv Campinas Unicamp, Dept Pathol, Fac Med Sci, BR-13083970 Campinas, SP, Brazil
Rogerio, F.
de Araujo Zanardi, V.
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Univ Campinas Unicamp, Dept Radiol, Fac Med Sci, BR-13083970 Campinas, SP, BrazilUniv Campinas Unicamp, Dept Pathol, Fac Med Sci, BR-13083970 Campinas, SP, Brazil
de Araujo Zanardi, V.
Ribeiro de Menezes Netto, J.
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Univ Campinas Unicamp, Dept Radiol, Fac Med Sci, BR-13083970 Campinas, SP, BrazilUniv Campinas Unicamp, Dept Pathol, Fac Med Sci, BR-13083970 Campinas, SP, Brazil
Ribeiro de Menezes Netto, J.
de Souza Queiroz, L.
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Univ Campinas Unicamp, Dept Pathol, Fac Med Sci, BR-13083970 Campinas, SP, BrazilUniv Campinas Unicamp, Dept Pathol, Fac Med Sci, BR-13083970 Campinas, SP, Brazil