Susac syndrome as an example of a rare vasculopathy

被引:4
|
作者
Olszanecka-Glinianowicz, Magdalena [1 ]
Hrycek, Antoni [2 ]
机构
[1] Med Univ Silesia, Div Pathophysiol, Katowice, Poland
[2] Med Univ Silesia, Dept Internal Autoimmune & Metab Dis, Katowice, Poland
关键词
encephalopathy; Susac syndrome; vasculopathy; HEARING-LOSS; MICROANGIOPATHY; BRAIN; RETINA; ENCEPHALOPATHY;
D O I
10.20452/pamw.612
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
Susac syndrome is a rare vasculopathy affecting small vessels of the brain, the retina and the cochlea. The pathogenesis of this syndrome is unknown. It is characterized by a triad of clinical symptoms, i.e. encephalopathy, visual disorders and hearing disorders. The aim of this work was to review available data about the clinical course, diagnosis and treatment of Susac syndrome.
引用
收藏
页码:80 / 82
页数:3
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