Endogenous lipoid pneumonia preceding diagnosis of pulmonary alveolar proteinosis

被引:8
|
作者
Antoon, James W. [1 ]
Hernandez, Michelle L. [2 ]
Roehrs, Phillip A. [3 ]
Noah, Terry L. [4 ]
Leigh, Margaret W. [4 ]
Byerley, Julie S. [1 ]
机构
[1] Univ N Carolina, Sch Med, UNC Hosp, Div Gen Pediat & Adolescent Med, 260 MacNider Bldg,CB 1593, Chapel Hill, NC 27599 USA
[2] Univ N Carolina, Sch Med, UNC Hosp, Div Allergy Immunol Rheumatol & Infect Dis, Chapel Hill, NC USA
[3] Univ N Carolina, Sch Med, Div Hematol & Oncol, UNC Hosp, Chapel Hill, NC USA
[4] Univ N Carolina, Sch Med, Dept Pediat, Div Pulmonol,UNC Hosp, Chapel Hill, NC USA
来源
CLINICAL RESPIRATORY JOURNAL | 2016年 / 10卷 / 02期
关键词
crazy paving pattern; interstitial lung disease; lipoid pneumonia; non-specific interstitial pneumonitis; pediatric pulmonology; pulmonary alveolar proteinosis; CHOLESTEROL GRANULOMAS; DISEASE;
D O I
10.1111/crj.12197
中图分类号
R56 [呼吸系及胸部疾病];
学科分类号
摘要
Pulmonary alveolar proteinosis (PAP) is an under-reported and under-diagnosed condition, with a high percentage of cases found on autopsy or late stage disease. The etiology of PAP includes genetic, primary (anti-granulocyte-macrophage colony-stimulating factor antibodies) and secondary (oncologic, rheumatologic, infectious, chemical and immunologic) causes. Here, we present the first reported pediatric case of endogenous lipoid pneumonia and non-specific interstitial pneumonitis preceding the development of PAP.
引用
收藏
页码:246 / 249
页数:4
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