MRI in the mild type of mucopolysaccharidosis II (Hunter's syndrome)

被引：1
|
作者：
Shinomiya, N
Nagayama, T
Fujioka, Y
Aoki, T
机构：
来源：
NEURORADIOLOGY | 1996年 / 38卷 / 05期
关键词：
Hunter's syndrome; mucopolysaccharidosis; magnetic resonance imaging; computed tomography; Virchow-Robin spaces;
D O I：
暂无
中图分类号：
R74 [神经病学与精神病学];
学科分类号：
摘要：
We report imaging findings in a 3-year-old boy with the typical mild type of Hunter's disease, MRI revealed multifocal large cyst- or spindle-like areas of increased and decreased signal in the white matter, including the corpus callosum on T1- and T2-weighted images, The white matter showed high signal on T2-weighted images, isointense with cerebrospinal fluid on all other pulse sequences. To our knowledge, these appearances have not been reported in this disorder, Deposition of mucopolysaccharide and/or glycolipid and increase in fluid content seem to be responsible.
引用
收藏
页码：483 / 485
页数：3
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