An update on the management of chronic inflammatory demyelinating polyneuropathy

被引:39
|
作者
Gorson, Kenneth C. [1 ]
机构
[1] St Elizabeths Med Ctr, Dept Neurol, Boston, MA 02135 USA
关键词
CIDP; demyelinating neuropathy; immune neuropathy; inflammatory polyneuropathy; IVIg; treatment;
D O I
10.1177/1756285612457215
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
Chronic inflammatory demyelinating polyneuropathy (CIDP) is an immune mediated disorder of the peripheral nervous system with clinical features that include weakness, sensory loss, imbalance, pain and impaired ambulation which may lead to substantial disability. This review highlights current treatment strategies for CIDP, how best to utilize proven therapies such as intravenous immunoglobulin, oral prednisone, pulse dexamethasone, and plasma exchange, and when and how to use alternative immunosuppressive agents when first-line therapies are ineffective or poorly tolerated.
引用
收藏
页码:359 / 373
页数:15
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