What is new in 2015 in dysimmune neuropathies?

被引:1
|
作者
Kuntzer, T. [1 ]
机构
[1] Univ Lausanne Hosp CHUV, Dept Clin Neurosci, Neurol Serv, Nerve Muscle Unit, 46 Rue Bugnon, CH-1011 Lausanne, Switzerland
关键词
Immune neuropathic syndromes; CIDP; Nodopathy; Dysimmune neuropathy; INFLAMMATORY DEMYELINATING POLYNEUROPATHY; MULTIFOCAL MOTOR NEUROPATHY; GUILLAIN-BARRE-SYNDROME; INTRAVENOUS IMMUNOGLOBULIN; PERIPHERAL-NERVE; CIDP; THERAPY; IMMUNOTHERAPY; ANTIBODIES; POLYRADICULONEUROPATHY;
D O I
10.1016/j.neurol.2016.03.010
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
This review discusses and summarizes the concept of nodopathies, the diagnostic features, investigations, pathophysiology, and treatment options of chronic inflammatory demyelinating polyradiculoneuropathy, and gives updates on other inflammatory and dysimmune neuropathies such as Guillain-Barre syndrome, sensory neuronopathies, small-fiber-predominant ganglionitis, POEMS syndrome, neuropathies associated with IgM monoclonal gammopathy and multifocal motor neuropathy. This field of research has contributed to the antigenic characterization of the peripheral motor and sensory functional systems, as well as helping to define immune neuropathic syndromes with widely different clinical presentation, prognosis and response to therapy. (C) 2016 Elsevier Masson SAS. All rights reserved.
引用
收藏
页码:779 / 784
页数:6
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