Metastatic alveolar soft part sarcoma of the kidney in a young female

被引:0
|
作者
Kumar, Shritosh [1 ]
Nayak, Brusabhanu [1 ]
Bharati, Vandna [2 ]
Kaushal, Seema [2 ]
Sharma, Mehar Chand [2 ]
机构
[1] All India Inst Med Sci, Dept Urol, New Delhi, India
[2] All India Inst Med Sci, Dept Pathol, New Delhi, India
关键词
D O I
10.4103/iju.iju_340_23
中图分类号
R5 [内科学]; R69 [泌尿科学(泌尿生殖系疾病)];
学科分类号
1002 ; 100201 ;
摘要
A 19-year-old female presented with left flank discomfort and swelling. Imaging revealed a large mass arising from the left kidney, and radical nephrectomy confirmed the diagnosis of alveolar soft part sarcoma (ASPS) based on histopathological and ultrastructural examination. Postoperatively, positron emission tomography-computerized tomography showed lung metastasis and renal bed recurrence. Sunitinib was initiated for metastatic ASPS. This case underscores challenges in diagnosing and managing ASPS, highlighting the role of tyrosine kinase inhibitors. Multidisciplinary care and vigilant follow-up are crucial for rare tumors such as ASPS.
引用
收藏
页码:65 / 67
页数:3
相关论文
共 50 条
  • [31] HISTOGENESIS OF ALVEOLAR SOFT PART SARCOMA
    MUKAI, M
    TORIKATA, C
    LABORATORY INVESTIGATION, 1985, 52 (01) : A45 - A46
  • [32] HISTOGENESIS OF ALVEOLAR SOFT PART SARCOMA
    KARNAUCHOW, PN
    MAGNER, D
    JOURNAL OF PATHOLOGY AND BACTERIOLOGY, 1963, 86 (01): : 169 - &
  • [33] ALVEOLAR SOFT PART SARCOMA OF THE TONGUE
    CETIK, F
    OZSAHINOGLU, C
    KIVANC, F
    SECINTI, E
    JOURNAL OF LARYNGOLOGY AND OTOLOGY, 1989, 103 (10): : 952 - 954
  • [34] Alveolar soft part sarcoma of the larynx
    Tahir Altuğ
    Ender İnci
    Melih Güven Güvenç
    Deniz Tuna Edizer
    Sergülen Dervişoğlu
    European Archives of Oto-Rhino-Laryngology, 2007, 264 : 445 - 449
  • [35] Cytopathology of Alveolar Soft Part Sarcoma
    Wakely, Paul E., Jr.
    McDermott, James E.
    Ali, Syed Z.
    CANCER CYTOPATHOLOGY, 2009, 117 (06) : 500 - 507
  • [36] ALVEOLAR SOFT PART SARCOMA OF THE UTERUS
    NOLAN, NPM
    GAFFNEY, EF
    HISTOPATHOLOGY, 1990, 16 (01) : 97 - 99
  • [37] ALVEOLAR SOFT-PART SARCOMA
    LIEBERMA.PH
    FOOTE, FW
    STEWART, FW
    BERG, JW
    JOURNAL OF THE AMERICAN MEDICAL ASSOCIATION, 1966, 198 (10): : 1047 - &
  • [38] ALVEOLAR SOFT PART SARCOMA OF THE VAGINA
    CARINELLI, SG
    GIUDICI, MN
    BRIOSCHI, D
    CEFIS, F
    TUMORI, 1990, 76 (01) : 77 - 80
  • [39] ALVEOLAR SOFT-PART SARCOMA
    RANEY, RB
    MEDICAL AND PEDIATRIC ONCOLOGY, 1979, 6 (04): : 367 - 370
  • [40] ALVEOLAR SOFT PART SARCOMA OF THE HAND
    TROUM, S
    FLOYD, WE
    JOURNAL OF HAND SURGERY-AMERICAN VOLUME, 1993, 18A (06): : 1016 - 1018