A rare case of scimitar syndrome with pulmonary arterial hypertension in an adult female

被引:0
|
作者
Liu, Yang [1 ,3 ]
Ruan, Weiliang [1 ]
Li, Ziye [1 ]
Wang, Hua [2 ]
Chen, Shenghai [1 ]
Ding, Yuhong [1 ]
Jin, Jianfeng [1 ]
机构
[1] Shaoxing City Keqiao Dist Hosp Tradit Chinese Med, Resp Dept, Shaoxing, Peoples R China
[2] Shaoxing City Keqiao Dist Hosp tradit Chinese Med, Special Inspection Dept, Shaoxing, Peoples R China
[3] Shaoxing City Keqiao Dist Hosp tradit Chinese Med, Resp Dept, Shaoxing 312030, Peoples R China
关键词
computed tomography angiography; pulmonary arterial hypertension; scimitar syndrome;
D O I
10.1002/pul2.12332
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
Scimitar syndrome is a rare congenital anomaly characterized by partial or total anomalous pulmonary venous drainage of the right lung to the inferior vena cava. We report a case of a 67-year-old female who presented with cough and dyspnea and was diagnosed with scimitar syndrome and pulmonary arterial hypertension based on comprehensive imaging and hemodynamic evaluation. This case highlights the importance of considering scimitar syndrome as a cause of pulmonary hypertension even in adult patients.
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页数:4
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