Streptococcal endarteritis associated with severe aortic coarctation

Bicuspid aortic valve and coarctation of the aorta are risk factors for infective endocarditis and endarteritis. We describe a case of a 4-year-old boy whose severe aortic coarctation was diagnosed only when he presented with endarteritis due to Streptococcus pneumoniae, which evolved into a mycotic pseudoaneurysm requiring urgent repair.