Current management of classic bladder exstrophy in the modern era

被引:3
|
作者
Morrill, Christian C. [1 ]
Haffar, Ahmad [1 ]
Harris, Thomas G. W. [2 ]
Crigger, Chad [1 ]
Gearhart, John P. [1 ]
机构
[1] Johns Hopkins Univ, Charlotte Bloomberg Childrens Hosp, Douglas A Canning MD Exstrophy Database Ctr, Sch Med,James Buchanan Brady Urol Inst,Div Pediat, 1800 Orleans St Suite 7204, Baltimore, MD 21287 USA
[2] Johns Hopkins Univ, Sch Med, Dept Plast & Reconstruct Surg, Baltimore, MD USA
关键词
Bladder exstrophy; Transitional urology; Congenitalism; QUALITY-OF-LIFE; COMPLETE PRIMARY REPAIR; SEXUAL HEALTH OUTCOMES; DELAYED PRIMARY REPAIR; FREE-FLAP PHALLOPLASTY; TERM-FOLLOW-UP; EPISPADIAS COMPLEX; PRIMARY CLOSURE; PENILE RECONSTRUCTION; NECK RECONSTRUCTION;
D O I
10.1186/s12301-023-00356-4
中图分类号
R5 [内科学]; R69 [泌尿科学(泌尿生殖系疾病)];
学科分类号
1002 ; 100201 ;
摘要
BackgroundClassic bladder exstrophy is a complex, multi-system congenital malformation affecting formation of the genitourinary system, pelvis, and abdominal wall.Main bodyHistorically children with this abnormality were consigned to poor outcomes and quality of life. Modern advancements in the diagnosis and management of this disorder have resulted in low mortality rates and shifted clinical focus toward optimizing quality of life.ConclusionModern techniques in addition to recent discoveries in the diagnosis and delayed management of this disorder have enabled high rates of urinary continence, genital cosmesis, and an improved quality of life. This is an updated overview of the pathology, diagnosis, and management of this rare disorder.
引用
收藏
页数:14
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