Interstitial lung disease and primary Sjogren syndrome: A case report

被引:0
|
作者
Athanasopoulou, Georgia [1 ]
Zakynthinos, Georgios [1 ]
Eleftheriou, Konstantinos [1 ]
Dima, Effrosyni [1 ]
Magkou, Christina [2 ]
Katsaounou, Paraskevi [1 ]
Kalomenidis, Ioannis [1 ]
机构
[1] Natl & Kapodistrian Univ Athens, Evaggelismos Hosp, Dept Crit Care & Pulmonol Med 1, Sch Med, Athens, Greece
[2] Evaggelismos Hosp, Dept Pathol, Athens, Greece
来源
PNEUMON | 2023年
关键词
interstitial lung disease; pulmonary hypertension; Sjogren syndrome;
D O I
10.18332/pne/161143
中图分类号
R56 [呼吸系及胸部疾病];
学科分类号
摘要
We present the case of a 28-year-old African man with multiple hospitalizations during the past two years due to worsening shortness of breath. The initial work-up revealed recurrent pulmonary embolism and interstitial lung disease (ILD). The diagnosis of primary Sjogren syndrome was established and a lung biopsy demonstrated cellular non-specific interstitial pneumonia (NSIP). Proper treatment of NSIP was partially effective and respiratory failure persisted, implying additional pathology to NSIP. Further evaluation revealed pulmonary hypertension that required treatment with pulmonary vasodilators.
引用
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页数:5
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