Flank Pain as a First Symptom of a Diffuse Midline Glioma

被引:1
|
作者
Bassa, Burc [1 ]
Battmann, Achim [2 ]
Craemer, Eva Maria [1 ]
Meyding-Lamade, Uta [1 ]
机构
[1] Krankenhaus NW Frankfurt, Dept Neurol, Frankfurt, Germany
[2] Krankenhaus NW Frankfurt, Dept Pathol, Frankfurt, Germany
关键词
Midline glioma; Spinal cord tumors; Acute paraparesis; K27M mutation; PROGNOSIS;
D O I
10.1159/000528311
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
Diffuse midline gliomas are a new entity in the WHO Classification of Tumors of the Central Nervous System, corresponding to grade 4 gliomas. The diagnostic pathognomonic feature is the presence of a H3K27M mutation. Although mainly seen in children, cases in adults have also been reported. The symptoms are highly variable and usually dependent on the location and extent of spinal cord compression.
引用
收藏
页码:1 / 5
页数:5
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