Severe and life-threatening onset of systemic lupus erythematosus

被引:0
|
作者
Martins, Ana [1 ,2 ]
Pimenta, Sofia [1 ,2 ]
Oliveira, Daniela [1 ,2 ]
Martins, Frederico [3 ]
Samoes, Beatriz [4 ]
Costa, Lucia [1 ]
机构
[1] Ctr Hosp & Univ Sao Joao, Dept Rheumatol, Porto, Portugal
[2] Univ Porto, Dept Med, Fac Med, Porto, Portugal
[3] Hosp Faro, Dept Nephrol, CHA, Faro, Portugal
[4] Ctr Hosp Vila Nova Gaia Espinho, Dept Rheumatol, Vila Nova De Gaia, Portugal
来源
REUMATOLOGIA CLINICA | 2023年 / 19卷 / 07期
关键词
Systemic lupus erythematosus; Macrophagic activation syndrome; Cyclosporin; MACROPHAGE ACTIVATION SYNDROME; DIAGNOSIS;
D O I
10.1016/j.reuma.2022.09.006
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
Macrophage activation syndrome (MAS) is a potentially life-threatening complication of rheumatic diseases. We report a unique case of a previously healthy 20-year-old female presenting with MAS as first presentation of systemic lupus erythematosus. Remission was achieved with hydroxychloroquine, intravenous methylprednisolone pulse followed by oral prednisolone and cyclosporine. However, the management of MAS is still challenging, and the mortality rate remains high. & COPY; 2022 Elsevier Espana, S.L.U. and Sociedad Espanola de Reumatologia y Colegio Mexicano de Reumatologia. All rights reserved.
引用
收藏
页码:402 / 403
页数:2
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