Systemic Amyloid A Amyloidosis Secondary to Xanthogranulomatous Pyelonephritis
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作者:
Habuka, Masato
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Niigata Prefectural Shibata Hosp, Div Nephrol, Shibata, JapanNiigata Prefectural Shibata Hosp, Div Nephrol, Shibata, Japan
Habuka, Masato
[1
]
Nishikiori, Mizusa
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Niigata Prefectural Shibata Hosp, Div Nephrol, Shibata, JapanNiigata Prefectural Shibata Hosp, Div Nephrol, Shibata, Japan
Nishikiori, Mizusa
[1
]
Oikawa, Chihiro
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Niigata Prefectural Shibata Hosp, Div Nephrol, Shibata, JapanNiigata Prefectural Shibata Hosp, Div Nephrol, Shibata, Japan
Oikawa, Chihiro
[1
]
Takahashi, Megumi
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Niigata Prefectural Shibata Hosp, Div Nephrol, Shibata, JapanNiigata Prefectural Shibata Hosp, Div Nephrol, Shibata, Japan
Takahashi, Megumi
[1
]
Sakamaki, Yuichi
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Niigata Prefectural Shibata Hosp, Div Nephrol, Shibata, JapanNiigata Prefectural Shibata Hosp, Div Nephrol, Shibata, Japan
Sakamaki, Yuichi
[1
]
Ogawa, Asa
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Niigata Prefectural Shibata Hosp, Div Nephrol, Shibata, JapanNiigata Prefectural Shibata Hosp, Div Nephrol, Shibata, Japan
Ogawa, Asa
[1
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Miyajima, Norio
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Niigata Prefectural Shibata Hosp, Div Urol, Shibata, JapanNiigata Prefectural Shibata Hosp, Div Nephrol, Shibata, Japan
Miyajima, Norio
[2
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Tanabe, Yasuhiko
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Niigata Prefectural Shibata Hosp, Div Cardiol, Shibata, JapanNiigata Prefectural Shibata Hosp, Div Nephrol, Shibata, Japan
Tanabe, Yasuhiko
[3
]
Honma, Keiichi
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Niigata Prefectural Shibata Hosp, Div Pathol, Shibata, JapanNiigata Prefectural Shibata Hosp, Div Nephrol, Shibata, Japan
Honma, Keiichi
[4
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Wakaki, Kunihiko
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Niigata Prefectural Shibata Hosp, Div Pathol, Shibata, JapanNiigata Prefectural Shibata Hosp, Div Nephrol, Shibata, Japan
Wakaki, Kunihiko
[4
]
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Yamamoto, Suguru
[5
]
Narita, Ichiei
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机构:
Niigata Univ, Kidney Res Ctr, Div Clin Nephrol & Rheumatol, Grad Sch Med & Dent Sci, Niigata, JapanNiigata Prefectural Shibata Hosp, Div Nephrol, Shibata, Japan
Narita, Ichiei
[5
]
机构:
[1] Niigata Prefectural Shibata Hosp, Div Nephrol, Shibata, Japan
[2] Niigata Prefectural Shibata Hosp, Div Urol, Shibata, Japan
[3] Niigata Prefectural Shibata Hosp, Div Cardiol, Shibata, Japan
[4] Niigata Prefectural Shibata Hosp, Div Pathol, Shibata, Japan
[5] Niigata Univ, Kidney Res Ctr, Div Clin Nephrol & Rheumatol, Grad Sch Med & Dent Sci, Niigata, Japan
systemic AA amyloidosis;
xanthogranulomatous pyelonephritis;
serum amyloid A;
NATURAL-HISTORY;
DISEASE;
D O I:
10.2169/internalmedicine.1806-23
中图分类号:
R5 [内科学];
学科分类号:
1002 ;
100201 ;
摘要:
The combination of systemic amyloid A (AA) amyloidosis and xanthogranulomatous pyelonephritis (XGP) resulting from a chronic urinary tract infection is extremely rare. We herein report a case of systemic AA amyloidosis secondary to XGP for which clinical remission developed after nephrectomy. To our knowledge, this is the first case report describing the clinical improvement of systemic AA amyloidosis secondary to XGP after nephrectomy in Japan. Clinicians should be aware of this uncommon combination and search for amyloid depositions in cases of XGP.