Impaired lung function in infants with primary ciliary dyskinesia: A pilot Czech study

被引:0
|
作者
Koucky, Vaclav [1 ,2 ,4 ,5 ]
Martinu, Vendula [1 ,2 ]
Koucky, Miroslav [3 ]
机构
[1] Charles Univ Prague, Dept Paediat, Prague, Czech Republic
[2] Univ Hosp Motol, Prague, Czech Republic
[3] Tech Univ Liberec, Fac Sci Humanities & Educ, Dept Math, Liberec, Czech Republic
[4] Charles Univ Prague, Fac Med 2, Dept Paediat, V Uvalu 84, Prague 5, Czech Republic
[5] Univ Hosp Motol, V Uvalu 84, Prague 5, Czech Republic
关键词
infant; infant lung function; primary ciliary dyskinesia; ventilation inhomogeneity;
D O I
10.1002/ppul.26863
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
引用
收藏
页码:1124 / 1127
页数:4
相关论文
共 50 条
  • [41] Growth and nutritional status, and their association with lung function: a study from the international Primary Ciliary Dyskinesia Cohort
    Goutaki, Myrofora
    Halbeisen, Florian S.
    Spycher, Ben D.
    Maurer, Elisabeth
    Belle, Fabien
    Amirav, Israel
    Behan, Laura
    Boon, Mieke
    Carr, Siobhan
    Casaulta, Carmen
    Clement, Annick
    Crowley, Suzanne
    Dell, Sharon
    Ferkol, Thomas
    Haarman, Eric G.
    Karadag, Bulent
    Knowles, Michael
    Koerner-Rettberg, Cordula
    Leigh, Margaret W.
    Loebinger, Michael R.
    Mazurek, Henryk
    Morgan, Lucy
    Nielsen, Kim G.
    Phillipsen, Maria
    Sagel, Scott D.
    Santamaria, Francesca
    Schwerk, Nicolaus
    Yiallouros, Panayiotis
    Lucas, Jane S.
    Kuehni, Claudia E.
    EUROPEAN RESPIRATORY JOURNAL, 2017, 50 (06)
  • [42] A Study on the Genetics of Primary Ciliary Dyskinesia
    Alsamri, Mohammed T.
    Alabdouli, Amnah
    Iram, Durdana
    Alkalbani, Alia M.
    Almarzooqi, Ayesha S.
    Souid, Abdul-Kader
    Vijayan, Ranjit
    JOURNAL OF CLINICAL MEDICINE, 2021, 10 (21)
  • [43] Impaired Growth during Childhood in Patients with Primary Ciliary Dyskinesia
    Svobodova, Tamara
    Djakow, Jana
    Zemkova, Daniela
    Cipra, Adam
    Pohunek, Petr
    Lebl, Jan
    INTERNATIONAL JOURNAL OF ENDOCRINOLOGY, 2013, 2013
  • [44] Impaired childhood growth velocity in patients with primary ciliary dyskinesia
    Svobodova, Tamara
    Djakow, Jana
    Zemkova, Dana
    Cipra, Adam
    Pohunek, Petr
    Lebl, Jan
    EUROPEAN RESPIRATORY JOURNAL, 2013, 42
  • [45] Is the sensitivity of primary ciliary dyskinesia detection by ciliary function analysis 100%?
    Pifferi, Massimo
    Bush, Andrew
    Montemurro, Francesca
    Pioggia, Giovanni
    Piras, Martina
    Tartarisco, Gennaro
    Di Cicco, Maria
    Chinellato, Iolanda
    Cangiotti, Angela M.
    Boner, Attilio L.
    EUROPEAN RESPIRATORY JOURNAL, 2013, 42 (04) : 1161 - 1161
  • [46] Lung Clearance Index in Primary Ciliary Dyskinesia and Bronchiectasis
    Irving, Samantha J.
    Davies, Jane C.
    Alton, Eric W. F.
    Bush, Andrew
    AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE, 2014, 189 (09) : 1147 - 1148
  • [47] Structural and functional lung disease in primary ciliary dyskinesia
    Santamaria, Francesca
    Montella, Silvia
    Tiddens, Harm A. W. M.
    Giddi, Guido
    Casotti, Valeria
    Maglione, Marco
    de Jong, Pim A.
    CHEST, 2008, 134 (02) : 351 - 357
  • [48] Recovery of baseline lung function after pulmonary exacerbation in children with primary ciliary dyskinesia
    Sunther, Meera
    Bush, Andrew
    Hogg, Claire
    McCann, Lauren
    Carr, Siobhan B.
    PEDIATRIC PULMONOLOGY, 2016, 51 (12) : 1362 - 1366
  • [49] LUNG SCINTIGRAPHY IN 22 PATIENTS WITH PRIMARY CILIARY DYSKINESIA
    MUNKNER, T
    PEDERSEN, M
    EUROPEAN JOURNAL OF RESPIRATORY DISEASES, 1983, 64 : 479 - 480
  • [50] Lung Clearance Index in Children with Primary Ciliary Dyskinesia
    Green, K.
    Buchvald, F.
    Marthin, J. K.
    Hanel, B.
    Gustafsson, P.
    Nielsen, K. G.
    AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE, 2010, 181