Malignant atrophic papulosis (Degos disease) with central nervous system involvement

被引:0
|
作者
Guo, Kundian [1 ]
Jiang, Chunxia [2 ]
Yan, Bo [1 ,3 ]
Hao, Xiaoting [1 ]
机构
[1] Sichuan Univ, West China Hosp, Dept Neurol, 37 Guoxue Rd, Chengdu 610041, Sichuan, Peoples R China
[2] Shenzhen Univ, Clin Med Acad, Dept Ophthalmol, Gen Hosp, Shenzhen, Guangdong, Peoples R China
[3] Chengdu Shangjin Nanfu Hosp, Dept Neurol, Chengdu, Sichuan, Peoples R China
基金
国家重点研发计划;
关键词
Atrophic papulosis; Degos disease; Central nervous system;
D O I
10.1007/s10072-023-07242-5
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
A 49-year-old man presented with a 2-year history of weakness and sensory disturbances in the bilateral lower extremities, vesicorectal dysfunction, and progressive gait disturbances. Brain MRI revealed multiple ischemic and hemorrhagic cortical/subcortical lesions with patchy enhancement involving the frontal and parietal lobes, suggesting the possibility of distal perforating arteries injury. Spine MRI revealed lesions of the cervical and thoracic spinal cord with associated enhancement. The diagnosis of malignant atrophic papulosis (Degos disease) with central nervous system involvement was prompted by the characteristic skin lesions.
引用
收藏
页码:1803 / 1805
页数:3
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