Malignant atrophic papulosis (Degos disease)

被引:0
|
作者
Xu, Qiuyun [1 ]
Lin, Mengting [1 ]
Zhang, Liangliang [1 ]
Chen, Suni [1 ]
Gong, Ting [2 ]
Cheng, Bo [1 ]
Ji, Chao [1 ]
机构
[1] Fujian Med Univ, Affiliated Hosp 1, Dept Dermatol, 20 Chazhong Rd, Fuzhou 350000, Fujian, Peoples R China
[2] Fujian Med Univ, Affiliated Hosp 1, Cent Lab, Fuzhou, Peoples R China
关键词
Malignant atrophic papulosis; Degos disease; Vasculopathy; Gastrointestinal involvement; Dermoscopic examination; Histopathological examination;
D O I
10.1111/ajd.13722
中图分类号
R75 [皮肤病学与性病学];
学科分类号
100206 ;
摘要
Malignant atrophic papulosis (Degos disease) is a rare syndrome of multiple-system vascular diseases with unknown etiology. It can affect the skin, gastrointestinal tract and central nervous system. Here, we report a 58-year-old woman with extensive porcelain-white atrophic papules. Based on the clinical manifestations, skin biopsy and colonoscopy, a diagnosis of malignant atrophic papulosis was confirmed.
引用
收藏
页码:E586 / E588
页数:3
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