Macrophage Activation Syndrome

被引：1
|
作者：
Nigrovic, Peter A. [1 ,2 ]
机构：
[1] Boston Childrens Hosp, Boston, MA 02115 USA
[2] Harvard Med Sch, Brigham & Womens Hosp, Boston, MA 02115 USA
来源：
ARTHRITIS & RHEUMATOLOGY | 2024年
关键词：
JUVENILE IDIOPATHIC ARTHRITIS; HEMOPHAGOCYTIC LYMPHOHISTIOCYTOSIS; T-CELLS; INTERFERON-GAMMA; SOLUBLE INTERLEUKIN-2-RECEPTOR; HLH; ETOPOSIDE; CHILDREN; CYTOTOXICITY; DYSFUNCTION;
D O I：
10.1002/art.43052
中图分类号：
R5 [内科学];
学科分类号：
1002 ; 100201 ;
摘要：
Macrophage activation syndrome (MAS) is a state of immune hyperactivation that can result in life-threatening multisystem end-organ dysfunction. Often termed a "cytokine storm," MAS occurs among the rheumatic diseases most typically in Still's disease but also in systemic lupus erythematosus and Kawasaki disease. MAS can also accompany infection, malignancy, and inborn errors of immunity. This review provides a practical, evidence-based guide to the understanding, recognition, and management of MAS in children and adults, with a primary focus on MAS complicating Still's disease.
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收藏
页数：13
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