Pediatric lymphoproliferative disorders associated with inborn errors of immunity
被引:2
|
作者:
Cheng, Jinjun
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机构:
Childrens Natl Hosp, Dept Pathol & Lab Med, Washington, DC USA
Childrens Natl Hosp, Ctr Canc & Blood Disorders, Washington, DC USA
Childrens Natl Hosp, Ctr Canc, Washington, DC USA
Childrens Natl Hosp, Immunol Res, Washington, DC USAChildrens Natl Hosp, Dept Pathol & Lab Med, Washington, DC USA
Cheng, Jinjun
[1
,2
,3
,4
]
Saldana, Blachy J. Davila
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h-index: 0
机构:
Childrens Natl Hosp, Ctr Canc & Blood Disorders, Washington, DC USA
Childrens Natl Hosp, Ctr Canc, Washington, DC USA
Childrens Natl Hosp, Immunol Res, Washington, DC USA
George Washington Univ, Sch Med & Hlth Sci, Washington, DC USAChildrens Natl Hosp, Dept Pathol & Lab Med, Washington, DC USA
Saldana, Blachy J. Davila
[2
,3
,4
,5
]
Chandrakasan, Shanmuganathan
论文数: 0引用数: 0
h-index: 0
机构:
Childrens Healthcare Atlanta, Aflac Canc & Blood Disorders Ctr, Atlanta, GA USAChildrens Natl Hosp, Dept Pathol & Lab Med, Washington, DC USA
Chandrakasan, Shanmuganathan
[6
]
Keller, Michael
论文数: 0引用数: 0
h-index: 0
机构:
Childrens Natl Hosp, Ctr Canc & Blood Disorders, Washington, DC USA
Childrens Natl Hosp, Ctr Canc, Washington, DC USA
Childrens Natl Hosp, Immunol Res, Washington, DC USAChildrens Natl Hosp, Dept Pathol & Lab Med, Washington, DC USA
Keller, Michael
[2
,3
,4
]
机构:
[1] Childrens Natl Hosp, Dept Pathol & Lab Med, Washington, DC USA
[2] Childrens Natl Hosp, Ctr Canc & Blood Disorders, Washington, DC USA
[3] Childrens Natl Hosp, Ctr Canc, Washington, DC USA
[4] Childrens Natl Hosp, Immunol Res, Washington, DC USA
[5] George Washington Univ, Sch Med & Hlth Sci, Washington, DC USA
[6] Childrens Healthcare Atlanta, Aflac Canc & Blood Disorders Ctr, Atlanta, GA USA
Inborn errors of immunity;
Lymphoproliferative disorder;
Lymphoma;
EBV;
WHO classification;
International consensus classification;
CELL TRANSPLANTATION;
LYMPHOMA;
DISEASE;
MUTATIONS;
DEFICIENCY;
LUNG;
LYMPHADENOPATHY;
CLASSIFICATION;
HYPERPLASIA;
PHENOTYPE;
D O I:
10.1016/j.clim.2024.110332
中图分类号:
R392 [医学免疫学];
Q939.91 [免疫学];
学科分类号:
100102 ;
摘要:
Both non-malignant and malignant lymphoproliferative disorders (LPD) are commonly seen in patients with inborn errors of immunity (IEI), which may be the presenting manifestations or may develop during the IEI disease course. Here we review the clinical, histopathological, and molecular features of benign and malignant LPD associated with IEI and recognize the diagnostic challenges.
机构:
Ctr Univ Saude ABC, Fac Med, Serv Referencia Doencas Raras, Imunol Clin, Sao Paulo, SP, BrazilCtr Univ Saude ABC, Fac Med, Serv Referencia Doencas Raras, Imunol Clin, Sao Paulo, SP, Brazil
Demaret Bardou, Maine Luellah
Henriques, Marina Teixeira
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机构:
Ctr Univ Saude ABC, Fac Med, Serv Referencia Doencas Raras, Imunol Clin, Sao Paulo, SP, BrazilCtr Univ Saude ABC, Fac Med, Serv Referencia Doencas Raras, Imunol Clin, Sao Paulo, SP, Brazil
Henriques, Marina Teixeira
Grumach, Anete Sevciovic
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h-index: 0
机构:
Ctr Univ Saude ABC, Fac Med, Serv Referencia Doencas Raras, Imunol Clin, Sao Paulo, SP, BrazilCtr Univ Saude ABC, Fac Med, Serv Referencia Doencas Raras, Imunol Clin, Sao Paulo, SP, Brazil
机构:
RIKEN Ctr Integrat Med Sci, Lab Transcript Regulat, 1-7-22 Suehiro Cho,Tsurumi Ku, Yokohama, Kanagawa 2300045, Japan
Tokyo Med & Dent Univ TMDU, Grad Sch Med & Dent Sci, Dept Pediat & Dev Biol, 1-5-45 Yushima,Bunkyo Ku, Tokyo 1138519, JapanRIKEN Ctr Integrat Med Sci, Lab Transcript Regulat, 1-7-22 Suehiro Cho,Tsurumi Ku, Yokohama, Kanagawa 2300045, Japan
Yamashita, Motoi
Morio, Tomohiro
论文数: 0引用数: 0
h-index: 0
机构:
Tokyo Med & Dent Univ TMDU, Grad Sch Med & Dent Sci, Dept Pediat & Dev Biol, 1-5-45 Yushima,Bunkyo Ku, Tokyo 1138519, Japan
Tokyo Med & Dent Univ TMDU, Adv Res Inst, Lab Immunol & Mol Med, 1-5-45 Yushima,Bunkyo, Tokyo 1138519, JapanRIKEN Ctr Integrat Med Sci, Lab Transcript Regulat, 1-7-22 Suehiro Cho,Tsurumi Ku, Yokohama, Kanagawa 2300045, Japan