A Cryptogenic Case of Fulminant Fibrosing Organizing Pneumonia

被引:7
|
作者
Kobayashi, Takehiko [1 ]
Kitaichi, Masanori [2 ,3 ,4 ]
Tachibana, Kazunobu [1 ,2 ]
Kishimoto, Yutaro [1 ,5 ]
Inoue, Yasushi [1 ]
Kagawa, Tomoko [1 ,2 ]
Maekura, Toshiya [1 ]
Sugimoto, Chikatoshi [2 ]
Arai, Toru [2 ]
Akira, Masanori [2 ,6 ]
Inoue, Yoshikazu [2 ]
机构
[1] Natl Hosp Org, Kinki Chuo Chest Med, Dept Internal Med, Sakai, Osaka, Japan
[2] Natl Hosp Org, Kinki Chuo Chest Med, Clin Res Ctr, Sakai, Osaka, Japan
[3] Natl Hosp Org, Kinki Chuo Chest Med, Dept Pathol, Sakai, Osaka, Japan
[4] Natl Hosp Org, Minami Wakayama Med Ctr, Dept Pathol, Wakayama, Japan
[5] Iwata City Hosp, Dept Resp Med, Iwata, Shizuoka, Japan
[6] Natl Hosp Org, Kinki Chuo Chest Med Ctr, Dept Radiol, Sakai, Osaka, Japan
关键词
cryptogenic organizing pneumonia (COP); fibrosing organizing pneumonia (FOP); rapidly progressive bronchiolitis obliterans organizing pneumonia; bronchoscopy; PROGRESSIVE BRONCHIOLITIS OBLITERANS; TRANSBRONCHIAL LUNG-BIOPSY; CLASSIFICATION; CYCLOSPORINE; DISEASE; BOOP;
D O I
10.2169/internalmedicine.56.7371
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
Cryptogenic organizing pneumonia (COP) generally responds well to corticosteroids with a favorable outcome. Rare cases of organizing pneumonia are rapidly progressive. Yousem et al. studied pathologic predictors of idiopathic bronchiolitis obliterans organizing pneumonia/COP with an unfavorable prognosis. Beardsley and Rassl proposed the name fibrosing organizing pneumonia (FOP). A 74-year-old female non-smoker presented with a 2-week history of dry cough followed by dyspnea and a fever. The clinical course was fulminant, but we successfully performed bronchoscopy. After the diagnosis of FOP, we treated the patient with mechanical ventilation and high-doses of steroids/immunosuppressants, which improved the disease.
引用
收藏
页码:1185 / 1191
页数:7
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