MYELOFIBROSIS AND SYSTEMIC LUPUS-ERYTHEMATOSUS - REVERSAL OF FIBROSIS WITH HIGH-DOSE CORTICOSTEROID-THERAPY

被引:0
|
作者
INOUE, Y
MATSUBARA, A
OKUYA, S
OKAFUJI, K
KAKU, K
KANEKO, T
机构
关键词
CORTICOSTEROID; MYELOFIBROSIS; SYSTEMIC LUPUS ERYTHEMATOSUS; THROMBOCYTOPENIA;
D O I
暂无
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
A case of myelofibrosis in association with systemic lupus erythematosus (SLE) is reported. Acute thrombocytopenia and a bleeding tendency developed in a 24-year-old woman with SLE. Bone marrow aspiration was unsuccessful due to myelofibrosis. Pulse therapy with methylprednisolone reversed both thrombocytopenia and myelofibrosis. A review of the literature revealed that the coexistence of SLE and myelofibrosis is a rare occurrence. Only 7 cases, to our knowledge, have ever been reported in detail. The present case is the 3rd in which myelofibrosis was reversed by corticosteroids.
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收藏
页码:32 / 36
页数:5
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