POLYCYSTIC LIVER-DISEASE IS NOT ALWAYS ASSOCIATED WITH POLYCYSTIC KIDNEY-DISEASE

被引:0
|
作者
SIMON, P
ANG, KS
CHARASSE, C
GHALI, N
CATROUX, B
HOUITTE, H
机构
来源
REVUE DE MEDECINE INTERNE | 1993年 / 14卷 / 10期
关键词
D O I
10.1016/S0248-8663(05)80154-7
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
Adult polycystic disease of the liver (APLD) and of the kidney (ADPKD) is considered to represent one entity. In 75 ADPKD kindreds with 259 affected members, ultrasonography and/or CT were performed in 186 (71.8%) from 64 kindreds (85.3%). We demonstrate that ADPKD with or without APLD are two separate phenotypes and suggest genetic heterogeneity of these two entities.
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页码:1037 / 1037
页数:1
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