POLYCYSTIC LIVER-DISEASE IS NOT ALWAYS ASSOCIATED WITH POLYCYSTIC KIDNEY-DISEASE

被引:0
|
作者
SIMON, P
ANG, KS
CHARASSE, C
GHALI, N
CATROUX, B
HOUITTE, H
机构
来源
REVUE DE MEDECINE INTERNE | 1993年 / 14卷 / 10期
关键词
D O I
10.1016/S0248-8663(05)80154-7
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
Adult polycystic disease of the liver (APLD) and of the kidney (ADPKD) is considered to represent one entity. In 75 ADPKD kindreds with 259 affected members, ultrasonography and/or CT were performed in 186 (71.8%) from 64 kindreds (85.3%). We demonstrate that ADPKD with or without APLD are two separate phenotypes and suggest genetic heterogeneity of these two entities.
引用
收藏
页码:1037 / 1037
页数:1
相关论文
共 50 条
  • [1] POLYCYSTIC KIDNEY-DISEASE ASSOCIATED WITH POLYCYSTIC OVARIAN SYNDROME
    SEGASOTHY, M
    NORAZLINA, MY
    ONG, PH
    JAMIL, M
    NEPHRON, 1992, 62 (04): : 482 - 483
  • [2] SEVERE POLYCYSTIC LIVER-DISEASE (PLD) IN 27 PATIENTS WITH AUTOSOMAL-DOMINANT POLYCYSTIC KIDNEY-DISEASE (ADPKD)
    CHAUVEAU, D
    LEMOINE, A
    SAUVANET, A
    BELGHITI, J
    VONS, C
    FRANCO, D
    GRUNFELD, JP
    NECKER, H
    BEAUJON, H
    JOURNAL OF THE AMERICAN SOCIETY OF NEPHROLOGY, 1995, 6 (03): : 718 - 718
  • [3] POLYCYSTIC KIDNEY-DISEASE
    BOSNIAK, MA
    AMBOS, MA
    SEMINARS IN ROENTGENOLOGY, 1975, 10 (02) : 133 - 143
  • [4] POLYCYSTIC KIDNEY-DISEASE
    SUKI, WN
    KIDNEY INTERNATIONAL, 1982, 22 (05) : 571 - 580
  • [5] POLYCYSTIC KIDNEY-DISEASE
    CHESTER, AC
    HARRIS, JP
    SCHREINER, GE
    AMERICAN FAMILY PHYSICIAN, 1977, 16 (06) : 94 - 101
  • [6] POLYCYSTIC KIDNEY-DISEASE
    RITZ, E
    DEUTSCHE MEDIZINISCHE WOCHENSCHRIFT, 1987, 112 (39) : 1516 - 1516
  • [7] POLYCYSTIC KIDNEY-DISEASE
    BOURQUIA, A
    RAMDANI, B
    JABRANE, AJ
    KHAJIJ, T
    ZAID, D
    REVUE DE MEDECINE INTERNE, 1989, 10 (04): : 313 - 318
  • [8] JAUNDICE ASSOCIATED WITH POLYCYSTIC LIVER-DISEASE
    WITTIG, JH
    BURNS, R
    LONGMIRE, WP
    AMERICAN JOURNAL OF SURGERY, 1978, 136 (03): : 383 - 386
  • [9] HYPERTENSION IN POLYCYSTIC KIDNEY-DISEASE
    HANSSON, L
    KARLANDER, LE
    LUNDGREN, W
    PETERSON, LE
    SCANDINAVIAN JOURNAL OF UROLOGY AND NEPHROLOGY, 1974, 8 (03): : 203 - 205
  • [10] POLYCYSTIC KIDNEY-DISEASE AND INFERTILITY
    VANDERLINDEN, EFH
    BARTELINK, AKM
    IKE, BW
    VANLEEUWAARDEN, B
    FERTILITY AND STERILITY, 1995, 64 (01) : 202 - 203