A GIANT CONGENITAL ORBITAL TUMOR - AN UNUSUAL PRESENTATION OF RETINOBLASTOMA

被引:1
|
作者
ZWAAN, CM
DEWAAL, FC
KOOLE, FD
MENKO, FH
VANDERVALK, P
SLATER, RM
SCHEFFER, H
VANWAVEREN, G
MOLL, AC
SCHOUTENVANMEETEREN, AYN
TAN, KEWP
机构
[1] FREE UNIV AMSTERDAM HOSP,DEPT CLIN GENET,AMSTERDAM,NETHERLANDS
[2] FREE UNIV AMSTERDAM HOSP,DEPT OPHTHALMOL,AMSTERDAM,NETHERLANDS
[3] FREE UNIV AMSTERDAM HOSP,DEPT PATHOL,AMSTERDAM,NETHERLANDS
[4] UNIV AMSTERDAM,ACAD MED CTR,INST HUMAN GENET,1105 AZ AMSTERDAM,NETHERLANDS
[5] UNIV GRONINGEN,DEPT MED GENET,9700 AB GRONINGEN,NETHERLANDS
[6] BOVEN IJ HOSP,DEPT PEDIAT,AMSTERDAM,NETHERLANDS
来源
MEDICAL AND PEDIATRIC ONCOLOGY | 1994年 / 23卷 / 06期
关键词
RETINOBLASTOMA; CONGENITAL TUMOR; CYTOGENETICS; NEUROBLASTOMA;
D O I
10.1002/mpo.2950230611
中图分类号
R73 [肿瘤学];
学科分类号
100214 ;
摘要
We report a case of an unusual giant congential tumor presenting in a newborn infant as a large exophytic mass emerging from the left orbit. After enucleation orbital recurrence developed within 14 days. No anti-tumor treatment was given and the child died at the age of 4 weeks. The histopathological and cytogenetical analysis of the tumor is presented. The tumor was diagnosed as a retinoblastoma but we could not exclude the possibility of a neuroblastoma. (C) 1994 Wiley-Liss, Inc.
引用
收藏
页码:507 / 511
页数:5
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