RECURRENT DISLOCATION OF THE PATELLA IN KABUKI MAKE-UP SYNDROME

被引:0
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作者
IKEGAWA, S
SAKAGUCHI, R
KIMIZUKA, M
YANAGISAKO, Y
TOKIMURA, F
机构
关键词
GENERALIZED LIGAMENTOUS LAXITY; KABUKI MAKE-UP SYNDROME; PATELLA; RECURRENT DISLOCATION; SKELETAL DYSPLASIA;
D O I
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中图分类号
R826.8 [整形外科学]; R782.2 [口腔颌面部整形外科学]; R726.2 [小儿整形外科学]; R62 [整形外科学(修复外科学)];
学科分类号
摘要
Three patients with Kabuki make-up syndrome (KMS) who had recurrent dislocation of the patella are reported. In all, dislocation of the patella developed in adolescence, and they had generalized ligamentous laxity and dysplasia of the patellofemoral joints. In two of the three patients, surgical intervention was required; the operation was successful in one, but yielded poor results in the other. In the third patient, cardiac complications precluded operation. Orthopedists should be aware of this possible complication when treating patients with KMS.
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页码:265 / 267
页数:3
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