Dental treatment of children with Angelman syndrome: a case report
被引:6
|
作者:
Murakami, Christiana
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机构:
Univ Sao Paulo, Pediat Dent, Sao Paulo, BrazilUniv Sao Paulo, Pediat Dent, Sao Paulo, Brazil
Murakami, Christiana
[1
]
Nahas Pires Correa, Maria Salete
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机构:
Univ Cruzeiro Sul, Pediat Dent, Sao Paulo, Brazil
Univ Sao Paulo, Orthodont & Pediat Dent Dept, Sao Paulo, BrazilUniv Sao Paulo, Pediat Dent, Sao Paulo, Brazil
Nahas Pires Correa, Maria Salete
[2
,3
]
Pires Correa, Fernanda Nahas
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机构:
Univ Sao Paulo, Sao Paulo, BrazilUniv Sao Paulo, Pediat Dent, Sao Paulo, Brazil
Pires Correa, Fernanda Nahas
[4
]
Nahas Pires Correa, Jose Paulo
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机构:
Univ Sao Paulo, Operat Dent, Sao Paulo, BrazilUniv Sao Paulo, Pediat Dent, Sao Paulo, Brazil
Nahas Pires Correa, Jose Paulo
[5
]
机构:
[1] Univ Sao Paulo, Pediat Dent, Sao Paulo, Brazil
[2] Univ Cruzeiro Sul, Pediat Dent, Sao Paulo, Brazil
[3] Univ Sao Paulo, Orthodont & Pediat Dent Dept, Sao Paulo, Brazil
[4] Univ Sao Paulo, Sao Paulo, Brazil
[5] Univ Sao Paulo, Operat Dent, Sao Paulo, Brazil
Angelman syndrome;
dental treatment of disabled people;
psychological aspects;
D O I:
10.1111/j.1754-4505.2008.00003.x
中图分类号:
R78 [口腔科学];
学科分类号:
1003 ;
摘要:
Angelman syndrome (AS) is a rare genetic neurological disorder. The main clinical characteristics of this syndrome are delayed neuropsychological development, intellectual disability, speech impairment, movement or balance disorder, and a behavioural uniqueness. The syndrome has oral manifestations such as diastemas, tongue thrusting, sucking/swallowing disorder, mandibular prognathism, a wide mouth, frequent drooling, and excessive chewing behaviour. The dental literature on the syndrome is scarce. The purpose of this paper is to describe the interesting aspects of the dental treatment of a child with AS.
机构:
Chulalongkorn Univ, Ctr Excellence Med Genom, Med Genom Cluster, Dept Pediat,Fac Med, Bangkok, Thailand
King Chulalongkorn Mem Hosp, Excellence Ctr Genom & Precis Med, Thai Red Cross Soc, Bangkok, ThailandPrince Songkla Univ, Dept Pathol, Fac Med, Hat Yai, Thailand
Kor-anantakul, Phawin
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机构:
Charalsawadi, Chariyawan
Worachotekamjorn, Juthamas
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机构:
Prince Songkla Univ, Dept Pediat, Fac Med, Hat Yai, ThailandPrince Songkla Univ, Dept Pathol, Fac Med, Hat Yai, Thailand
Worachotekamjorn, Juthamas
Limprasert, Pornprot
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机构:
Siam Univ, Fac Med, Bangkok, ThailandPrince Songkla Univ, Dept Pathol, Fac Med, Hat Yai, Thailand
机构:
Hosp Municipal Infantil Menino Jesus, Sao Paulo, BrazilHosp Municipal Infantil Menino Jesus, Sao Paulo, Brazil
Lopes, Alessandra G. D.
Celestino, Camila S. H.
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Hosp Municipal Infantil Menino Jesus, Sao Paulo, BrazilHosp Municipal Infantil Menino Jesus, Sao Paulo, Brazil
Celestino, Camila S. H.
Barros, Tiago T. A.
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机构:
Hosp Municipal Infantil Menino Jesus, Sao Paulo, Brazil
Hosp Sirio Libanes, Sao Paulo, BrazilHosp Municipal Infantil Menino Jesus, Sao Paulo, Brazil
Barros, Tiago T. A.
Fevereiro, Aline G.
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Hosp Municipal Infantil Menino Jesus, Sao Paulo, BrazilHosp Municipal Infantil Menino Jesus, Sao Paulo, Brazil
Fevereiro, Aline G.
Gejer, Debora H.
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Hosp Municipal Infantil Menino Jesus, Sao Paulo, BrazilHosp Municipal Infantil Menino Jesus, Sao Paulo, Brazil
Gejer, Debora H.
Oliveira, Fernando M. F.
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Hosp Municipal Infantil Menino Jesus, Sao Paulo, BrazilHosp Municipal Infantil Menino Jesus, Sao Paulo, Brazil
Oliveira, Fernando M. F.
Brasil, Jamile M.
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Hosp Municipal Infantil Menino Jesus, Sao Paulo, BrazilHosp Municipal Infantil Menino Jesus, Sao Paulo, Brazil
Brasil, Jamile M.
Bossolan, Rosely M.
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Hosp Municipal Infantil Menino Jesus, Sao Paulo, BrazilHosp Municipal Infantil Menino Jesus, Sao Paulo, Brazil
Bossolan, Rosely M.
Pinto, Gabriela C. C.
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Hosp Municipal Infantil Menino Jesus, Sao Paulo, BrazilHosp Municipal Infantil Menino Jesus, Sao Paulo, Brazil
Pinto, Gabriela C. C.
Santos, Ana C. E. Z.
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Hosp Municipal Infantil Menino Jesus, Sao Paulo, BrazilHosp Municipal Infantil Menino Jesus, Sao Paulo, Brazil
Santos, Ana C. E. Z.
Divan, Luis A.
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Hosp Municipal Infantil Menino Jesus, Sao Paulo, BrazilHosp Municipal Infantil Menino Jesus, Sao Paulo, Brazil
Divan, Luis A.
Alves, Ingrid A. B.
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Hosp Municipal Infantil Menino Jesus, Sao Paulo, BrazilHosp Municipal Infantil Menino Jesus, Sao Paulo, Brazil
Alves, Ingrid A. B.
Oliveira, Danielle B. L.
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机构:
Univ Sao Paulo, Inst Ciencias Biomed, Dept Microbiol, Sao Paulo, Brazil
Hosp Israelita Albert Einstein, Sao Paulo, BrazilHosp Municipal Infantil Menino Jesus, Sao Paulo, Brazil
Oliveira, Danielle B. L.
Machado, Rafael R. G.
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Univ Sao Paulo, Inst Ciencias Biomed, Dept Microbiol, Sao Paulo, BrazilHosp Municipal Infantil Menino Jesus, Sao Paulo, Brazil
Machado, Rafael R. G.
Thomazelli, Luciano M.
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Univ Sao Paulo, Inst Ciencias Biomed, Dept Microbiol, Sao Paulo, BrazilHosp Municipal Infantil Menino Jesus, Sao Paulo, Brazil
Thomazelli, Luciano M.
Hiyane, Meire I.
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机构:
Univ Sao Paulo, Inst Ciencias Biomed, Dept Imunol, Sao Paulo, BrazilHosp Municipal Infantil Menino Jesus, Sao Paulo, Brazil
Hiyane, Meire I.
Brelaz-Abreu, Leonilia
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机构:
Hosp Sirio Libanes, Sao Paulo, BrazilHosp Municipal Infantil Menino Jesus, Sao Paulo, Brazil
Brelaz-Abreu, Leonilia
Braganca-Jardim, Elayne
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机构:
Hosp Sirio Libanes, Sao Paulo, BrazilHosp Municipal Infantil Menino Jesus, Sao Paulo, Brazil
Braganca-Jardim, Elayne
Heinen, Leticia B. S.
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机构:
Hosp Sirio Libanes, Sao Paulo, BrazilHosp Municipal Infantil Menino Jesus, Sao Paulo, Brazil
Heinen, Leticia B. S.
Barrientos, Anna C. M.
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Hosp Municipal Infantil Menino Jesus, Sao Paulo, BrazilHosp Municipal Infantil Menino Jesus, Sao Paulo, Brazil
Barrientos, Anna C. M.
Mau, Luciana B.
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Hosp Municipal Infantil Menino Jesus, Sao Paulo, BrazilHosp Municipal Infantil Menino Jesus, Sao Paulo, Brazil
Mau, Luciana B.
Camara, Niels O. S.
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机构:
Univ Sao Paulo, Inst Ciencias Biomed, Dept Imunol, Sao Paulo, BrazilHosp Municipal Infantil Menino Jesus, Sao Paulo, Brazil
Camara, Niels O. S.
Bueno, Daniela F.
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机构:
Hosp Municipal Infantil Menino Jesus, Sao Paulo, Brazil
Hosp Sirio Libanes, Sao Paulo, BrazilHosp Municipal Infantil Menino Jesus, Sao Paulo, Brazil
Bueno, Daniela F.
Amano, Mariane T.
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Hosp Sirio Libanes, Sao Paulo, BrazilHosp Municipal Infantil Menino Jesus, Sao Paulo, Brazil