GENETICALLY DETERMINED HETEROGENEITY OF C1 ESTERASE INHIBITOR IN PATIENTS WITH HEREDITARY ANGIONEUROTIC EDEMA

被引:251
|
作者
ROSEN, FS
ALPER, CA
PENSKY, J
KLEMPERER, MR
DONALDSON, VH
机构
来源
JOURNAL OF CLINICAL INVESTIGATION | 1971年 / 50卷 / 10期
关键词
D O I
10.1172/JCI106708
中图分类号
R-3 [医学研究方法]; R3 [基础医学];
学科分类号
1001 ;
摘要
引用
收藏
页码:2143 / +
页数:1
相关论文
共 50 条
  • [21] ACTION OF COMPLEMENT IN HEREDITARY ANGIONEUROTIC EDEMA - ROLE OF C]1-ESTERASE
    DONALDSON, VH
    ROSEN, FS
    JOURNAL OF CLINICAL INVESTIGATION, 1964, 43 (11): : 2204 - +
  • [22] RESTRICTION-FRAGMENT-LENGTH-POLYMORPHISM OF THE C1 INHIBITOR GENE IN HEREDITARY ANGIONEUROTIC-EDEMA
    CICARDI, M
    IGARASHI, T
    KIM, MS
    FRANQI, D
    AGOSTONI, A
    DAVIS, AE
    JOURNAL OF CLINICAL INVESTIGATION, 1987, 80 (06): : 1640 - 1643
  • [23] USE OF PURIFIED C1 ESTERASE INHIBITOR IN PATIENTS WITH HEREDITARY ANGIOEDEMA
    LAXENAIRE, MC
    AUDIBERT, G
    JANOT, C
    ANESTHESIOLOGY, 1990, 72 (05) : 956 - 957
  • [24] Caesarean section in a parturient with C1 esterase inhibitor deficiency (angioneurotic oedema)
    Minville, V
    Saada, J
    Cartron, G
    Legac, YT
    Desprats, R
    ANNALES FRANCAISES D ANESTHESIE ET DE REANIMATION, 2006, 25 (03): : 315 - 316
  • [25] A DE-NOVO DELETION IN THE C1 INHIBITOR GENE IN A CASE OF SPORADIC HEREDITARY ANGIONEUROTIC-EDEMA
    ARIGA, T
    HOSHIOKA, A
    KOHNO, Y
    SAKAMAKI, T
    MATSUMOTO, S
    CLINICAL IMMUNOLOGY AND IMMUNOPATHOLOGY, 1993, 69 (01): : 103 - 105
  • [27] Effect of C1 esterase inhibitor in hereditary angioedema treatment
    Gurmen, Ekim Saglam
    Dogan, Serkan
    Sert, Eren
    Dikmetas, Cesareddin
    Hussein, Sennaz
    AMERICAN JOURNAL OF EMERGENCY MEDICINE, 2017, 35 (06): : 942.e5 - 942.e6
  • [28] C1 esterase inhibitor autoantibodies in hereditary angioedema (HAE)
    Varga, L
    Füst, G
    Visy, B
    Harmat, G
    Karádi, I
    Farkas, H
    MOLECULAR IMMUNOLOGY, 2003, 40 (2-4) : 223 - 223
  • [29] SYNTHESIS OF C1 INHIBITOR IN FIBROBLASTS FROM PATIENTS WITH TYPE-I AND TYPE-II HEREDITARY ANGIONEUROTIC-EDEMA
    KRAMER, J
    KATZ, Y
    ROSEN, FS
    DAVIS, AE
    STRUNK, RC
    JOURNAL OF CLINICAL INVESTIGATION, 1991, 87 (05): : 1614 - 1620
  • [30] CONSUMPTION OF C1 INHIBITOR BY CRYOPRECIPITATE IN A PATIENT WITH ACQUIRED ANGIONEUROTIC-EDEMA
    SUNDEL, RP
    GELFAND, JA
    ROSEN, FS
    DAVIS, AE
    CLINICAL RESEARCH, 1988, 36 (03): : A577 - A577